Ectodermal uye fibrous dysplasia. itsvo dysplasia

Under dysplasia (rakashandurwa kubva muchiGiriki sezvo dys - kuramba; wplasis - dzidzo) rinoreva chakaipa uye kukanganisa kukura chero nhengo. Ichi - a seboka izwi rinofukidza chero kutyorwa.

Fibrous dysplasia anoreva zvirwere skeletal ezvinhu, uye kunoratidzwa muna kuti pfupa rinenge kuchatsiviwa fibrous tishu. Izvi deforms mapfupa. The chikuru chinokonzera chirwere ichi ndicho chakaita bundu kwacho, iyo rinotanga mwana, uye ipapo anotanga mberi. Fibrous dysplasia rinowanzova vakadzi.

chirwere wandei classifications. The inonyanya Unit ndechokuti, zvichienderana padanho kuwanda ane pathological kwacho:

• monoossalnaya fibrous dysplasia kunokanganisa pfupa rimwe chete;
• poliossalnaya - kuchinjai kuchengetwa mapfupa akawanda (kazhinji anopararira kurutivi rumwe rutivi rwomuviri, uye kazhinji unowanikwa pauduku).

Chimiro chirwere rokutanga kunokanganisa cranial pfupa, chipande, mapfupa tubular (refu) mucheto. Wechipiri - Nenguva iyo vanopfuura makumi mashanu kubva muzana vose mapfupa marangwanda.

Huru yematambudziko zvinosanganisira kakawanda mitswe, izvo nokukurumidza coalesce, asi akanatsiridzwa tisawirirane mu mapfupa, uyewo sarcoma.

Fibrous dysplasia chero kurapwa havagoni kuva, chete vachibatsira matanho (nokuisazve mapfupa curettage, osteotomy), uye kugadzwa zvinodhaka kuti anobatsira marwadzo anogona.

Ectodermal dysplasia unosanganisira vakawanda zvirwere uye syndromes (anenge 100), musimboti unova kuvapo zvemamiriro kugadzira nomukaka ectoderm. The chiratidzo chokutanga - kuvapo hyperthermia, iyo kana vakaratidza, uye kakawanda kurwiswa kunogona kutungamirira rwakavhunika upi kukura zvedzidzo, kana rufu.

Unogona kusarudza zvinotevera mhando uye dzavo zviratidzo.

Angidroticheskaya anotanga kuoneka mune vacheche, mukomana uye anoramba hwose. Huru zvinhu ndiwo:

• nhaka zvirwere;
• deformation simba kwemeno;
• kuvapo slowdown iri nzara;
• mucosal atrophy (huro, muromo, mhino);
• ari kwokunze nechitarisiko chakafanana mwana varwere vane vachiberekwa njovhera.

Symptomatic kurapwa anopiwa. Hazvitenderwi: mazororo kumaodzanyemba nyika, basa inopisa uye namakemikari zvinomera.

Gidroticheskaya ekzodermalnaya dysplasia kunoratidzwa nokuchinja emichindwe, inotsika, bvudzi kukura. Pakurapa rinowanzoshandurwa chinotarisirwa vhitamini "A" kwekunze uye mukati, kunyoroveswa ruomba uye keratolytics. Kuwedzera kune izvi, kushandisa: enzymatic zvinoreva Methyluracilum, anabolic steroids, zingi, amino acids uye biostimulants.

Renal dysplasia ane mhando dzakawanda kuti dzakasiyana:

• morphological kuratidzwa (cystic uye nyore);
• Localization (cortico-medullary, medullary uye cortical);
• Kupararira - nhamba, segmental, zvatichiri).

The chikuru chinokonzera chirwere ichi vari masero okutodza uye teratogenic nechinzwano zvokunze simba pamusoro mudumbu. Saka, achishandisa chirwere vari vachiberekwa malformations, iyo, pasinei mhando, kutungamirira vasanyanye itsvo kukura, anorura kukura parenchyma, chinokosha rutapudzo mitambo yayo.

Kurapa chirwere ichi symptomatic uye kakawanda kacho kana pane chiratidzo nokuda transplantation ari nhengo.

Kazhinji, dysplasia unotora boka zvirwere iyo inosanganisira zvemamiriro kukura ane nhengo kana yose hurongwa. Kazhinji, chikuru chinoita - kuvabereki uye vachiberekwa zvinhu.

Treatment riri symptomatic, kana kurumbidza vari ive nhengo nokuisazve kana pfupa.