Chii Morgagni-Stewart-Morel chirwere?

Syndrome pamusoro Morgagni-Stewart-Morel, Photo kuratidzirana chinogona kuonekwa munyaya ino, kwava kushoma - vanhu miriyoni imwe kurwara zvose chete zana namakumi mana. Uyezve, pamaitiro, nyanzvi vanosangana kazhinji ne "nezvimedu" nehosha, nokuti chirwere hwapedyo kucherechedzwa kwemakore akawanda, uye zviratidzo panguva aimhanya siyana. Varwere vanofanira aongororwe hakuna chiremba ari chirwere vasati richiratidzwa zvakazara uye kuona chaiyo zvawanikwa.

The akaoma mamiriro hosha rinosvika, kana anoumba munhu pathological kusingarapiki kuchinja mumuviri. Pashure paizvozvo, kubatsira murwere zvisingaiti.

nyaya

Syndrome pakati Morgagni-Stewart-Morel yakatsanangurwa kwazvo muna 1762, apo rokuItari pathologist Morgagni akazarura chitunha vakadzi makumi mana uye akawana thickening pakati mukati frontal mapfupa ndiro. Panguva iyoyowo, akaona kufutisa uye kunyanya muviri bvudzi. Morgagni akawana nezviratidzo dyidzana uye anorondedzerwa zvakadzama ake zvaakacherechedza. Gare gare, musi mubatanidzwa zviratidzo vakacherechedza Morel uye Stewart vakakwanisa kuwedzera kunotoda mufananidzo siyana chetsinga uye vepfungwa kuratidzwa.

Chii chirwere

Morgagni-Stewart-Morel chirwere - chirwere umo dzakaonekwa frontal hyperostosis yomukati mapfupa ndiro, kufutisa uye nezvimwe kwemakemikari anobudiswa uye metabolic zvirwere. Kurwara mu ruzhinji rwakavapo vakadzi, kunyanya pashure pemakore makumi mana, asi dzimwe nguva pachena uye matatu. Pakati vanhurume chirwere anenge zvikasaitika, isingawanzopotswi kunze.

Etiology uye pathogenesis

Disease Morgagni-Stewart-Morel - urwere, pathogenesis uye etiology iyo vane chete tsananguro. Vamwe vanyori vanodavira kuti zvokurwara ndiye kuvabereki uye pachishandiswa autosomal kureva mhando. Pane mafungiro kuti chirwere ari chokuita X-chromosome. Paiva zviitiko apo chirwere vakatambura zvizvarwa zvina, runonyanya vakadzi.

Kune kure zviitiko chirwere kuratidzwa nevanhu. Asi havana nguva dziri kure, uye sayenzi haisati anozivikanwa sei maperembudzi kuburikidza murume mutsetse. Vamwe vakatenda kuti chirwere kakawanda kuonekwa vakadzi panguva kubereka. Asi Data vaunganidza pamusoro nguva, akaisa mashoko aya kupinda mubvunzo.

The chirwere chinogona kuitika nokuda zvirwere (kunyanya sinusitis), neuroinfections uye zvinorwadza kukuvara uropi. Kwakawanikwa Morgagni-Stewart-Morel chirwere castrates vakadzi vakambova kuvhiyiwa. Zvimwe zvaidiwa chirwere ingangoumbwa pashure kenza kurapwa.

Paiva zviitiko apo hosha vakanga dzakaonekwa pavarwere vane:

• uterine myoma;
• sklerokistoz ovaries;
• Kuramba galactorrhea;
• pasikarudzi infantilism.

Morgagni-Stewart-Morel urwere: zvokurwara

Kana chirwere haisi chete mukobvu yomukati frontal mapfupa ndiro, asi pano neapo dzakaonekwa hyperostosis musoro uye fronto-occipital nharaunda. Kune vakawanda kuchinja roga mune kwemakemikari anobudiswa mumasero. Kuwedzera eosinophilic uye masero basophilic. Tanga adenomatous kuwanda (thyroid, adrenal cortex uye t. D.).

zviratidzo

Kana munhu akawanikwa Morgagni-Stewart-Morel urwere, pane nezviratidzo zvinoverengeka kuti zvaizobatsira nayo:

• Varwere vanotanga kuona nguva nomusoro.
• Kufutisa, kunyanya abdominal munharaunda.
• Skin anoramba zvisingatomboiti ruvara, asi kakawanda kuoneka pyoderma uye vachichema eczema.
• Kazhinji pane raidudzwa hypertrichosis.
• On ganda anozivikanwa pastoznost vanotanga kuzvimba makumbo yakaderera, rinowanika akrozianoz.
• Tsandanyama netesa.
• Pane kuchinja kumwoyo uye kufema zvomukati (mwoyo kuwedzera miganhu, pane kusanzwa pasi uye mwoyo kukundikana).
• The katsika hupere, catarrh rokumusoro kufema turakiti uye bronchopneumonia.
• Kuchinja kwemakemikari anobudiswa mumasero noruzhinji zvinhu vane. Exchange angava kuipa, hwakawedzera kana shoma.
• Ungaderedza carbohydrate shiviriro. Kazhinji chirwere cheshuga kunoratidzwa zvakajeka.

• Anetseka kumwedzi. In pamuviri, munguva iyi murwere ezvinhu kuipa.
• Kune huta uye chirwere chepfungwa. Vanoratidza pachavo muchimiro mupfungwa lability, kushatirwa, kushaya hope uye tsika mwoyo.
• Internal frontal hyperostosis ndiro rinowanzoshandiswa thickened dehenya mapfupa. Mune zvimwe zviitiko, kunyange kuwedzera ukuru Turkish Chigaro.

chirwere

Morgagni-Stewart-Morel chirwere chinogona kuita pamusoro muviri nenzira dzakasiyana. Kazhinji kunobva mwero kufutisa. Raidudzwa ane zvakarwadza chaizvo upenyu anotarisirwa:

• nebasa mwoyo yakaoma;
• nokuda kuunganidza mafuta kuitika myocardium uye pericardium;
• chepamusoro ari diaphragm;
• kufamba kweropa, uye akabatana atherosclerosis uye BP kusimukira mwoyo kukundikana, inova chikonzero yokuremara;
• kana murwere chete chirwere vane zvakawanda uye chirwere cheshuga, ipapo anotanga munhu metabolic nyonganyonga, iyo inotungamira kwete chete kune vasanyanye kunyatsoshanda, asi kunoderedza upenyu anotarisirwa.

mabatiro

Zvinoita here kubvisa urwere Morgagni-Stewart-Morel? Pakurapa chirwere chiri kunyanya kudya assignable chirwere cheshuga zvakafanana uye kufutisa. Zvokudya inofanira kuva pasi-mafuta, mukuru-mapuroteni, vhitamini uye chicherwa munyu. Zvokudya zvinoderedza uwandu makabhohaidhiretsi uye mafuta. Diet Baranov iri basa kunyanya.

Mukuwedzera, mishonga rinoitwa masaja uye basa mumuviri kudzidzisa kurovedza kuderedza tsandanyama simba uye kuvandudza peripheral kufamba kweropa. Kana murwere ane mwoyo kukundikana, pakurapa chirwere yakaitwa diuretics kardiopreparatami uye t. D.