UtanoZvirwere uye Conditions

Aplasia - a zvokurwara kuti anogona kukanganisa chero nhengo

Aplasia - kuratidzwa fetus malformations, iyo runoratidzwa pasina chero muviri chikamu kana tishu zvikamu. zvokurwara Izvi kusiyaniswa kubva hypoplastic panguva iyo muviri uve mucheche kana kuderedzwa kukura uye vasingadadi kwomuzvarirwo mamiriro.

Ndokusaka pane zvokurwara

Zvinofanira kucherechedzwa kuti aplasia - a vachiberekwa chirwere kuti kunoitika nokuda nezvainoita fetus zvakananga kana zvisina kunanga kuburikidza raamai muviri mumuviri, zvemakemikari uye utachiona zvinhu. Ivo, kuita pamusoro gametes vabereki kana madzitateguru avo, anogona kukonzera chromosomal abnormalities pamwe kusavapo ane nhengo kana tishu.

Nenzira, imwe undeveloped imwe nhengo iri embryo iri rinenge voga uye anotungamira kazhinji rufu chokuita nezvimwe muviri. Somuenzaniso, muna pasina ureteric chipande kunoitika yechipiri renal aplasia, uye m. P.

A vendu-kure musi, pashure iyo zvinorondedzerwa zvikanganiso zviri embryo handichakwanisi kuva, - ndiwo mwedzi intrauterine upenyu chokutanga.

Zvinoumba nezvekugadzirwa zvokurwara

hakuna nharaunda iri risingagoni kuchengetwa aplasia muvanhu. Izvi pathological mamiriro mumwe aiwanzopiwa wokushanda nhengo yemanyorero kunokonzera chimwe hypertrophy (aplasia rimwe kwemakemikari anobudiswa mumasero kungaita hypertrophy vamwe). Saka, pane yokutsiva, kuti muripo kurasika mabasa.

Kazhinji hapana chikamu muviri, akadai aplasia pakati ari corpus callosum kana olfactory uropi (chirwere inonzi arinentsefaliey), etc. Aplasia of zvinyama anowanzodanwa kuonekwa mumusoro. Panguva iyi mucheche akaberekwa dzakaonekwa rakaremara, izvo kazhinji asingadi kupfuudza 5 cm. Asi mamiriro yakadaro zvabatanidzwa riri kwakadzama Somuenzaniso ave mutemo, zvinyama aplasia, panyaya embryo asina kuvharirwa slits (t. N. Dizarfiya).

Zvemamiriro kukura mapfupa tishu

Sezvo ari zviitiko pamusoro apa, aplasia mapfupa ari kure muchimiro apo neapo. Saka, kana zvakadaro chirwere ari murwere fibula kupfupiswa muzvidimbu hwapedyo equinovarus rutsoka wakarebesa (pamucheto pamberi panguva vanomutswa, uye kuruvanze - akadarikira), curved tibia, hapana mhuru uye peroneal tsandanyama.

Aplasia munhu zviitiko zvakanyorwa zvokurapa nhengo dzomuviri, zvinowanza nemakumbo dzevanhu. Izvi zvinogona kuva kusava mumwe kana kupfuura minwe kana yose ruoko kana rutsoka. Kakawanda kushayikwa nzira nokuda honokono, mupambare, mafudzi, chidya, pamberi tsoka kana ruoko.

Aplasia yeDehenya uye uropi

Kana zvatichiri aplasia yeDehenya mapfupa, izvo mushonga Anonziwo "fenestrated dehenya", Yakaumbwa kuburikidza urema vane dzakasiyana kukura uye chimiro. Asi periosteum (fibrous Kamudzira rinofukidza pfupa) uye ganda iri nzvimbo urema izvi zviripo. Ivo dziri kunyanya mune parietal uye frontal kumatunhu.

Kana rusvava hapana mapfupa dehenya, kazhinji navo ipapo wakanyorova aplasia (It Anonziwo anencephaly). zvokurwara Iri 100% zvinouraya. Uyezve, 75% vana vachiri kufa utero, uye vamwe vanorarama hapana anopfuura 5 Mazuva azvarwa.

Kunyange kuvazivisa nyaya yokuberekwa muUnited States muna 1992, mumwe musikana ane chirwere chakadaro, uyo akararama makore 2 uye 174 mazuva. Kufema uye kushanda zvomukati mumuviri wake rinoitwa akachengetedzwa uropi hunde. Asi, zvakadaro, musikana nguva nenguva chokuita kuti unomubatsira kufema uyewo zvichiitika nematambudziko kutungamirira ayo chemabhazi.

Aplasia of dumbu uye nyinyo

Zviitiko underdevelopment kana pasina dumbu, fallopian sepombi uye nyinyo - kashoma nazvo abnormality. Vakadzi vane nazvo, haagoni mimba kana kuti mwana wako.

Dambudziko riri dzakaonekwa rinowanzova vasvika nechekare kuyaruka. Kwachiremba Woman kuunza zvichemo pamusoro kushaya kumwedzi uye (pasina ari nyinyo), hazvibviri zvounzenza upenyu. Panyaya iyi, murwere kazhinji anodzokororwa kwomuzvarirwo muviri marongerwo uye zvakanaka kunyatsobudirira yechipiri kurara maitiro.

Kana murwere ane rushoma aplasia pamusoro nyinyo, zvinogona kunyunyuta pamusoro pamwedzi nasal ropa, zamu unyoro, uye kuswedera kurwadza ari dzakaderera mudumbu, izvo pamwe kuunganidza kumwedzi aibuda, sezvo water drainage kana chirwere haigoni zita.

Fani kwakadaro kunotungamirira nebundu idzodzo - vanonzi hematocolpos. Pavanenge vachikura, nechepazasi abdominal marwadzo arching kuoneka unopinza, uye kana suppuration iiswe precipitates tembiricha rinobuda, nokusika wakakodzera mamiriro ezvinhu sepsis. The murwere iyi inoratidza kukurumidza kuvhiyiwa.

Kana mapundu ose dumbu haisi hapana nzira, sezvo pasina muviri, kusunungura ropa.

Aplasia - hazvina nguva dzose rufu

Sei muviri womunhu aplasia akasiyana nhengo, nyama kana muviri zvikamu zvakasiyana. Dzimwe mhando aplasia (pasina Hemisférios Cerebrais, mwoyo tsandanyama, vose netsvo, uye zvichingodaro. N.) haawirirani upenyu. Vamwe vanogona kukonzera chakakomba dysfunction muviri, uye hapana kuvhiya kuchaita kurufu murwere (diaphragmatic heniya , kana Hirschsprung chirwere).

Asi pasina chikamu kana zvose rimwe gumbo, uyewo aplasia pamusoro dumbu, izvozvo inowirirana upenyu. A chete hangaiwa undeveloped muviri, akadai yaitsigira divi renal aplasia, dzimwe nguva zvakazara ndanyarara hangu hypertrophy rimwe, uye nokudaro anogona akaora unooneka kumarudzi murwere upenyu.

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