Utano, Mushonga
Cerebellar hypoplasia: Zvinokonzera, Zviratidzo neMarapirwo
Hapana kusiya panowanikwa chero chirwere. Asi mune zvimwe zviitiko hosha kachitanga mudumbu uye mwana pakuzvarwa yakaratidza yakasiyana zvokurwara. Mumwe chirwere yakadaro cerebellar hypoplasia - chirwere chinobata mwana muuropi.
tsananguro
Cerebellum - chikamu uropi, riri shure nharaunda uye zvinokosha chezvinonhuwira epfungwa. muviri Iri basa Kufambisa ari kufamba, tsandanyama inzwi, uye kukwanisa kuchengeta kunyatsofunga. Cerebellar Hypoplasia honye achiperekedzwa vasanyanye rimwe kana maviri nhengo dzayo.
zvikonzero
Cerebellar hypoplasia ari akura - migumisiro kukodzera fetus, uye zvinokonzera chirwere ichi vari midzi Mararamiro mukadzi pamuviri. Pane zvinhu zvinoverengeka zvikuru kuti kungamutsawo chirwere.
- Kushandiswa doro.
Kupfuura zvinhu zvinokuvadza zviri murwiyo doro ndiro panyaya iyi. Kwenguva yakareba kunokuvadza panoparadzana mwoyo fetus nechepakati tsinga kutsamwisa paumbwe siyana anomera. Uyewo, panyaya iyi anokwanisa kuparadza dzinongoitika chipingamupinyi kuti kunodzivirira zvirwere zviri CNS, rakapinza muruoko muviri kuburikidza muropa. Kazhinji, kudhakwa panguva pamuviri rinokusha utano fetus parumananzombe.
- Kusvuta.
Kusiyana nezvinofungwa nevakawanda inokanganisa pamusoro azvarwa haana chikakananda uye zvimwe zvine chepfu anoumba mudzanga. Vanogona kukonzera malformation pamusoro Neural chubhu, uye saka fetus uropi uye musana. Kana kuputa panguva pamuviri cerebellar hypoplasia akanyorwa kakawanda.
- Kushandiswa kwezvinodhaka.
Zvinodhaka kunogona tsinga somukadzi ane pamuviri, uye mwana, saka wavo unoshandiswa zvachose hakubvumidzwi nguva dzose. Kwakadaro zvinhu kukonzera kusingarapiki kwazvinoita muviri, izvo pakupedzisira inotungamirira kurufu.
- Negashiro simba zvinodhaka.
zvinodhaka zvakawanda hazvibvumidzwe kushandiswa panguva yepamuviri. nzira yavo basa chete kana chakakomba chokunamata. Muchirwisa colour kuti hasha yezvokurapa kurapa zvingamuka hypoplasia zviri cerebellum ari mudumbu.
- Kuonana nemwaranzi.
Radioactive isotopes vanowanzotevedzera kuunganidza ari Líquido mvura uye placenta, izvo zvingaita kuti DNA kunotouraya mwana. Irradiation kana urefu kugara munzvimbo dzakakwirira nemwaranzi yomuropa hwakazara yematambudziko ngozi amai vanepamuviri uye mwana.
- Zvirwere zvinotapuriranwa.
Cerebellar hypoplasia zvingaitika mune chiitiko kuti mukadzi ane pamuviri achatora ichi chirwere zvinoita nyore sezvinoita gwirikwiti. Kutaura zvazviri, chirwere ichi nemavhairasi ngozi kwazvo. Kana chirwere rokutanga trimester, vanachiremba vakawanda vanoti kugumisa pamuviri, sezvo nengozi abnormalities ari mudumbu chaizvo. At akazotevera zvokukura vakadzi basa mishonga, asi zviri chete kubudirira 50% nyaya.
Zvinonzi zvakare ngozi mukuru toxoplasmosis, izvo zvinogona vakanonga kana uchikurukura vanorwara katsi, nemakonzo uye shiri. chirwere ichi kwete chete ane inokanganisa fetus, asi zvose zvinogona zvikonzere kubva kwepamuviri.
Kuwedzera pamusoro zvose kwezvikonzero, unofanira aparadzane kutaura zvokudya anokuvadza, izvo akabatana nevamwe zvinhu kunogona kukanganisa nzira pamuviri.
zviratidzo
Hypoplasia of cerebellar vermis mwana achabatsirwa kutyorwa zhinji pamuviri mabasa. Nyanzvi ziva zvinotevera zviratidzo:
- tremor (kudedera) musoro, okumusoro migumo;
- Kutaura nehasha, ndiko kuti, mwana kutaura zvakawanda sezvinoita yelping;
- Bato mbudzana anorasikirwa kumeso kwavo vova sechisina musoro;
- vana vane cerebellar hypoplasia kukura zvikuru zvishoma nezvishoma, kureva, ugare, famba uye kutaura vanotanga paya pane vezera ravo;
- Tsandanyama of hunde uye maoko nemakumbo uncoordinated kwakaderedza - nekuda ichi, simuka kana pasi mwana anova rakaoma zvikuru;
- Vana vakadaro zvakaoma chaizvo kuramba nechiyero, zvose kumira chinzvimbo uye agere;
- Bato pasina zvinoyamura kwakaoma zvisingaiti, asi kana vanhu vachiri kukwanisa kudzidza kufamba, gait rake kwazvo isiriyo;
- variko nyonganyonga iri anotsvedzerera tsandanyama ose viscera;
- vanhu vane cerebellar hypoplasia kazhinji vanotambura zvinetso zviri kufema mabasa;
- vana achangoberekwa tikafunga maperembudzi kazhinji kuchengetwa kusanzwa kana upofu.
The chiratidzo chinonyanya pachena cerebellar hypoplasia ari mwana - shaky, Kuzungunuka gait uye kutyora spatial nemunhu. Uyewo, vana dehenya saizi iduku zvikuru pane dzose, nokuti uropi vane zvishoma pane vana utano. Zvavakanga vachiyaruka saizi Chokwadi, kuwedzera, asi deformation remusoro arege vachiri kuramba.
Cerebellar hypoplasia mberi mumakore 10 oupenyu yomwana yokutanga, ipapo ezvinhu ake kudzikamiswa uye vanachiremba varayire vanotsigirana kurapa.
Diagnostics
Kazhinji, maperembudzi dzakaonekwa panguva yepamuviri nokuisa Ultrasound Diagnostics. Tevera mwana akataura anoratidza wetsinga. Anogona mishonga kurapwa kana vapore maitirwe ezvinhu.
mabatiro
Zvinosuruvarisa cerebellar hypoplasia anoonekwa hosha isingarapiki, uye vana vanoberekerwa nawo, kashoma kurarama kusvika gore. Matanho All vakatakudzwa kubva nemwana, zvainanga kudzorera vakarasika mashandiro uye containment chirwere chacho. Nzira kurapwa dzinosanganisira:
- muchiitwa zvainanga kukura co-kugadzwa;
- masaja;
- kuramba kutaura makirasi chiremba wechikadzi achindidzidzisa kutaura, mumwe chiremba;
- uyewo nevana Zvinokurudzirwa kakawanda sezvinobvira kukurukura uye Zimbabwian mavari akasiyana-siyana mabasa aunofarira, akadai kupenda kana Kurumi kuti kuva yakanaka motokari chigunwe.
dziviriro
Kudzivirira zvirwere inzira utano woupenyu mai nezveramangwana. Panguva pamuviri, unofanira kuona chiremba vasati kushandiswa chipi zvinodhaka, uye kubvisa zvachose hwako doro, fodya, zvinodhaka, uye zvichingodaro. D.
chirwere Chero nyore kudzivirira pane kurapa. Naizvozvo, kana mukadzi ari zvakakodzera kuzvitarisira apo akatakura mwana, ngozi abnormalities iri yekudyidzana ipfupi.
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