UtanoZvirwere uye Mamiriro

Ichthyosis yeganda: zvinokonzera, zviratidzo, kurapa

Rimwe boka rezvirwere rakatarirwa nemishonga, iyo inokonzerwa nekushandurwa kwepamusoro pechando cheganda panzvimbo yemagetsi. Pamusana pekuputsa, ganda rinosangana nedzimwe shanduko uye rinova rakafanana nezviyero zvehove. Ichi chirwere chizvarwa uye chinogona kuzviratidza pane imwe nguva yemunhu, pasinei nemadzinza, zvepabonde uye zvehupenyu hwevanhu. Ichthyosis inogona kuratidzika isina simba uye haibvumiri murwere chero matambudziko akasiyana, uye inogona kuva nehasha uye inotungamirira kurufu. Ichthyosis yeganda uye ichthyosis-sezvirwere zvine uwandu hwemhando uye, zvinosuruvarisa, zvakajairika uye zvakaoma kubata. Vakawanda vanotungamirira mabhakato ekurapa vari kushanda kuitira kuti zvishoma nezvishoma vadzivirire chirwere uye kuita kuti upenyu huve nyore kune varwere.

Ichthyosis chii?

Kuongorora maitiro echirongwa che stratum corneum ichthyosis. Zvinokonzera zviitiko zvaro zvinokonzerwa nekuputsika mune mazita ekuberekwa kwevabereki kana vabereki vose, iko-mu X chromosome. Kune zvirwere zvakawanda zvinoratidzika pachazvo uye zvinoita seychthyosis, asi chaizvoizvo hazvisi. Saka, hazvina kukodzera kutyisa kana pane zviratidzo zvakafanana. Chirwere chechokwadi chinogona kuonekwa chete nemumwe nyanzvi, uye zvirwere zvizhinji zveganda zvakafanana nazvo zvinogona kupora zvakabudirira. Ichthyosis yeganda uye zvirwere zve-ichthyosis zvine marudzi akawanda, asi mushonga unovatsanangurira mumapoka akawanda. Zvimwe pamusoro peumwe neumwe wavo - zvakawanda.

Ordinary ichthyosis

Iyo inonziwo "vulgar ichthyosis," ndiyo imwe yemhando dzakawanda kwazvo. Chirwere ichi chinoratidzika pazera remakore, asi, kusiyana nemamwe maitiro, hachivhiringidze vana kusvika pamwedzi mitatu yemakore.

Chirwere chinoshungurudza chinoshanda panguva yekuyaruka kwomurwere, uye izvi zvinenge makore gumi nemakore. Kana imwe nzvimbo yemhomhoni yemunhu yakasimbiswa, pane kugadziriswa mumamiriro ezvinhu eganda. Dzimwe zororo dzinouya mumwaka wezhizha, asi nekunaya kunopisa chirwere chinotanga kufambira mberi. Vakomana nevasikana vane mikana yakafanana vanogona kukura chirwere ichi. Ichthyosis inowanzoendeswa kubva kune anotakura (mumwe wevabereki) kumwana. Chirwere chacho chinotevera murwere muupenyu hwose, mamiriro acho anogona kuvandudza uye kuipa.

Zviratidzo zvezvinonyadzisa ichthyosis

Vulgar ichthyosis ine zita rakadaro nekuda kwekuti iye anoita seanozviisa pachena. Chirwere ichi chinokanganisa ganda rechiso, matama, huma uye miromo kunyanya. Ganda rinofukidzwa nediki shoma zviyero, zvakanyatsosiyaniswa neziso. Kuonekwa kwavo uye chimiro chavo zvakafanana negorosi yegorosi, nokuti kazhinji ichthyosis yeganda rinonzi "kurega pityrias". Nzvimbo dzakakanganiswa hazviwanzorevi kubwinya kana kuputika, asi ganda rinooma uye rinopisa. Chirwere hachigadziri bvudzi kana misumari yemurwere mukuru uye zvinokonzera kusazvidya mwoyo.

Chiso chinongova nzvimbo yepakutanga yenzvimbo yacho, nekufamba kwenguva kuwedzera kwaenda, asi zvimwe zvikamu zvemuviri zvave zvichitambudzwa. Kazhinji aya aya mabvi uye nehota mapepa, maruva uye nzvimbo yakaderera kumashure, dzimwe nguva maziso. Ichthyosis yakadaro haina kuchinja, kusiyana nemamwe marudzi, nzvimbo inogadzirisa nzvimbo uye nzvimbo dzine mapundu makuru akacheka. Maererano nehutano hwechirwere chechirwere uye ukuru uye chimiro chezviyero, kazhinji ichthyosis yeganda yakakamurwa kuva mhando dzakasiyana: nyore ichthyosis, xeroderma, serpentine, acicular, yakasviba uye inopenya (pearl) ichthyosis.

Zvinetso zvinogadzirisa

Vana vaduku nevechiri kuyaruka vari kuipa kupfuura ichthyosis. Zvikonzero zvinokanganisa nhengo nemitemo yemuviri.

  • Mwana wacho anokura zvishoma nezvishoma uye anowana uremu, anotarisa angular, kukanganisa mupfungwa dzinobudirira kunogoneka.
  • Kunowedzera sebum secretion nekukutuka, semugumisiro - chimiro chebvudzi rakaputsika, vanogona kuwira kunze. Nail mahwendefa anova akajeka, akaonda uye ane brittle.
  • Kuzvidzivirira kusina simba, uye saka vana vanowanzorwara nehutachiona uye huputi.
  • Kusvibiswa kwemetabolism uye utachiona hunoita, kushandiswa kwehomoni.
  • Cholesterol inomuka muropa, iyo inogona kutungamirira pamwoyo uye zvirwere zvevascular.
  • Yakagadzirwa "hupofu husiku" -mamiriro ezvinhu umo vanhu vasingasanisi zvinhu murima.

Zvose izvi zvinetso zvinonyanya kuoneka munguva yechando. Kunyatsotarisirwa kunofanira kupiwa kune zvakakodzera kudya uye kuchena. Kufamba mumhepo itsva uye sunbathing kunobatsira.

Ichthyosis inowanzo muitiro wakawandisa

Dendaase ichthyosis muhuwandu hwakawanda hunoratidzwa mukuratidzwa kwakasimba kweganda kunotarisana mumuviri wose uye kunobata zvepabonde: vanomumiririri vevarume chete vanorwara nefomu iyi. Vasikana vashoma vanorwara, asi ivo vanotakura. Kuva mai, vanoendesa chirwere kuvana vavo, avo vanozotumira chromosome yavo kune vanasikana vavo. Saka zvinogona kuenderera mberi nokusingaperi.

Kune musikana, chirwere chinopfurikidza chinogona kupedza kuparara. Maitiro akadaro haawanzoitiki uye anogona kuitika chete kana vabereki vake vose vaine utachiona, uye ivo vachapfuura nekusakadza kwekromosome yekasikana. Chirwere chacho chakaoma kwazvo, vasikana vakadaro havasati vasara.

Zviratidzo mumamiriro akawandisa

Kazhinji kacho chikafu chinoputika, vhudzi rinova rakapfava, rinowira kunze, kuraswa kwebvudzi kunogona kuitika. Zviyero zvakakura uye zvakakomba, zvakasiyana nehuwandu hwemavara, zvine mumvuri wakaita. Varwere vanotambura nokuputsa kwemuviri. Ikoko kunogona kutyora kwepafu system uye kukura kwepfungwa, iyo cornea yemaziso inova yakajeka, uye mamiriro ekurapa haawanzwisisiki.

Congenital ichthyosis mune zvakaoma fomu

Ichthyosis is congenital - iyo yakaoma kwazvo chirwere, inogona kuitika nenzira yakanyoro kana yakaoma. Nhamba yekupona yakanyanya kuduku, vana vanofa maawa akawanda mushure mokuberekwa. Muzviitiko zvisingaiti, mwana anogona kuchengetedza. Chirwere chacho chinoshandurwa kune mamwe maitiro, mu erythroderma, somuenzaniso. Mune zviitiko zvisingawanzoitiki, izvo zvakarurama zvinogona kunzi chishamiso, chirwere chacho chinopera zvachose nezera uye hachigoni kumvhiringidza munhu.

Zviratidzo zvemafomu akaoma

Congenital ichthyosis muvana inoratidzirwa mumatambudziko akawanda uye kusagadzikana. Vana vakadaro vanoberekwa nguva isati yasvika, nehope shoma. Ganda recheche rinoshanduka zvachose uye rinofanana nehobho inoputika, uye kubva kwavari inobudisa ropa.

Pane imwe nguva apo kukura kweganda mumwana kunopwanyika, nhengo dzakasara, maviri uye muchembera zvinoramba zvichikura zvakanaka. Ganda harisi kuvhara, rinobata uye rinoshandura mazinga akabatanidzwa kunze. Chiso uye muviri wose wemwana zvakanyatsonaka uye vanofunga kutarisa kwechisikigo.

Chikonzero chekufa kwepamusoro muzvisikwa zvinobva pamusana pokuti mhuka yakakonta inokura uye inokwevera kana kuvhara zvachose nhengo dzinokosha. Mwana achangoberekwa haagoni kufema uye kudya, nhengo dzomukati dzine zviremera mukugadzirisa, chirwere chinowanikwa. Vana vakadaro vanonziwo "Harlequins", uye chirwere ichi "Harlequin chiratidzo".

Congenital ichthyosis mufomu runyoro

Kana ichthyosis iri kuberekwa inowedzera muine unyoro (benzi), ipapo mwana anowana mukana wekurarama. Zvisikwa zvinokonzerwa nekératinized hazvikure zvakasimba, sepamutambo wakaoma. Nhengo dzomukati, kunyange kana dzakashata, dzinokwanisa kuita basa ravo rinokosha.

Zviratidzo zvechimiro chinyoro

Ichthyosis muvana inogona kukanganisa ganda rose kana zvimwe nzvimbo. Munzvimbo dzakadaro ganda rinoshandura ruvara rutsvuku, zvinodada zvinonzwika pasi payo, kunyanya munzvimbo dzinogadzirirwa ganda. Nzvimbo dzechipatara pane chiso chinogona kusvibisa kuonekwa, kutenderera maziso kana nzvimbo yemuromo nemhino. Asi kune mikana yekupona kwevana vakadaro.

Ichthyosis mu "chimiro" chimiro

Ichthyosis yakadaro yeganda dzimwe nguva inopesana nemapuranga follicles. Inowanikwa kune dzimwe nzvimbo apo ganda rakakotama (mabvi, zvigunwe zvisikwa). Iyo foci yakafukidzwa nemavhuvhu maduku, ayo akafukidzwa nemakona makuru, akajeka emuvara wepepuru.

Kudzivirira

Ichthyosis chirwere cheganda chisingagoni kudziviswa, asi zvinokwanisika kufanotaura kuberekwa kwevana vane chirwere. Paiva nenzvimbo dzakawanda dzekugadzirira mhuri, kupa mazano kune vanonzi geneticists. Nyanzvi dzichafungisisa zvose zviratidzo, kunyanya kana vakaroorana vechidiki kana hama dzavo vane maitiro echthyosis. Genetics ichafananidza nzira uye njodzi dzekugoneka kwekugadzirisa kwehutano hwakaoma hwehutachiwana mumucheche uye huchapa mazano pamusoro pekuronga kwemucheche. Kana njodzi dzakakwirira, vakaroorana vakadaro vanogona kurairwa kuti vasiye kuberekwa kwechecheche. Asi, chero zvingave, chisarudzo chichingovimba chete kune vakaroorana.

Kurwara kwe ichthyosis muhutu hwakaoma chirwere chinotyisa kwazvo. Kufa kwevana vachangobva kuberekwa kunoda kusvika 100%. Kunyangwe kana mwana akagona kurarama, hazvigoneki kuti hupenyu hwehupenyu hwake hunogona kunzi hutendere. Mwana akadaro haagoni kukura zvakajairika. Achave akatarisa kune zvirwere zvakasiyana-siyana zvinokonzera, kufamba kwose kunokonzera kutambura nemarwadzo. Vakaroorana vanofanira kuratidza mutoro uye havaregereri mazano evarapi.

Kurapa

Wakamboongororwa ne ichthyosis here? Nzira yekurapa chirwere ichi? Dermatologists, geneticists uye vanachirwere vane hutachiona hwehutachiona vanobata uye vanotungamirira chirwere chechirwere chacho. Kuzvidemba zvakadzama, chirwere ichi chinoreva zvirwere zvegeneti, uye hazvibviri kubvisa zvachose. Mishonga inokwanisa chete kugadzirisa hutano hwehutano hwepamusoro pamwero wakakodzera uye munzira dzose zvinogona kudzivirira kuonekwa kwezvirwere. Zvisikwa nemafuta anonyorera uye anoporesa nzvimbo dzakakanganiswa dzeganda, varwere vachamanikidzwa kushandisa muhupenyu hwose.

Chirwere che ichthyosis chinosanganisawo mupfungwa. Zvichida iwe unoda rubatsiro rwechiremba wepfungwa, uye kutsigirwa kwevanhu vepedyo kunokosha zvikuru. Kurambwa kwevanhu kunogona kudzvinyirira mamiriro ezvinhu akaoma evanhu. Vana vanofanira kutaura nevezera ravo. Zvakakosha kutsanangurira vana kuti chirwere ichi hachina kupararira uye hachina ngozi kwavari.

Kusurukirwa kunofanira kuchengetedzwa. Zvokudya zvinofanira kuva zvepamusoro-grade. Tora sunbathing, asi iva nechokwadi chokuti usadziye kupisa kwezuva uye kupisa. Kuratidza kushamba mumvura yegungwa kana kushambidza negungwa munyu. Zvakakosha kuomerera kune mararamiro ane hutano uye, nechinetso chiduku, tsvaka kubatsirwa navanachiremba. Utachiona hushoma kwazvo, iyo yakawira muhupenyu husina simba, hunogona kukura nokukurumidza kuva chirwere chinogara chakasimba nematambudziko.

Nzira nzira dzekurapa yechchyosis

Vanhu vanoporesa vanhu vanopa mazano mazhinji kune avo vanotambura necheka reganda. Izvo zvose zvakasiyana uye zvinotarisirwa kuita zvishoma nezvishoma kubvisa chirwere chechirwere uye kuderedza kusagadzikana. Zvisinei, rangarira, tevera mazano evanhu vane mafungiro asina kunaka kumishonga, vanofanira kungwarira. Kana mbuya vari mumusika vachinyatsoputira mishonga "kubva kune sludge ye ichthyos yeSceniman", iyo isiripo mune zvakasikwa, zviri nani kugara kure ne "intern" yakadaro. Asi mune mishonga yevanhu kune zvakakosha zvakanakira mazano. Chaizvoizvo, iyo teas uye mabhedha pamishonga decoctions. Kunewo mapepa emafuta edzimba, ayo anorongedzerwa pakugadzirisa muviri, kupora maitiro nekugadzirisa ganda. Izvo zvose zvinosanganisira zvisikwa zvechisikigo, uye hazvisi zvakaoma kuzvigadzirira kumba. Zvichida, iwe uchazvisarudzira iwe pachako maitiro akawandisa anoshanda uye akareruka.

Geneticists uye laboratories munyika dzakawanda dziri kushanda pakuwana mushonga kune vanhu vanotambura nezvirwere zvepabonde. Zvinotarisirwa kuti pane panaaa inowanikwa nokukurumidza, uye isu tichakwanisa kubvisa vanhu zvechirwere chisingafadzi uye chinotyisa chakanaka.

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