UtanoZvirwere uye Conditions

Marble mapfupa chirwere: zvinokonzera, zviratidzo, kurapwa, dziviriro

Marble chinhu vachiberekwa zvokurwara chirwere kuti kunoratidzwa diffuse osteosclerosis vakawanda mapfupa skeletal uye kuchinja zvakadzama karusiyamu-phosphorus muviri. The chirwere apo neapo. Wakatanga kurondedzerwa muna 1904 by chiremba wokuGermany uye radiologist Albers-Schoenberg (Albers-Schonberg NE). Marble chirwere kunoitika zvachose vose zera Categories, munyika yose pamusoro nyika, zvakafanana mune aroorane.

The chirwere ane nhamba anoreva zvakafanana - vachiberekwa osteosclerosis, osteopetrosis, uye dysplasia giperostaticheskaya Albers-Schonberg chirwere. Regai kunyonganisa machena chirwere uye chirwere inonzi "dzemabhura ganda." Kana machena mapfupa chirwere ari marangwanda anotanga kubudisa mamwe tsindirana fuma, uyewo ari medullary Canal kachitanga munhu batana pfupa. A machena anonzi vachiberekwa ganda vazonevroz midziyo paganda, kazhinji zvichiitika vana hworatidza pachayo reticular makwapa pamusoro neganda rinokwanisa kucheneruka ruvara pashure richipedza. Mushure achidziya ari chiratidzo nokupera. Zvinoitawo kunoitika nedzevakuru machena ganda ane mutete chiedza ganda vane matambudziko nemidziyo ropa.

The etiology chirwere ichi harizivikanwi. Kazhinji anozivikanwa Muzviitiko hosha ine machena mhuri hunhu uye chakasvitswa kubva kumarudzi namarudzi. Rake chirwere zita machena chikwereti rinokosha mufananidzo maekisirei pamusoro marangwanda, izvo runotaurwa kuva homogeneity kujairika uye unopinza mapfupa arambe achirema, uyewo kushaya mapfupa mamiriro. Kunenge kuti Mapfupa yemabhura.

Pane zvimiro zviviri chirwere machena:

- inoyerera pasina inooneka zvekuchipatara zviratidzo, akaonekwa bedzi X-ray ongororo;

- kunooneka pacharo mu muduku, wakareva zviratidzo.

The chikuru chepfungwa chirwere ndiye anoramba kana rushoma nokuomesa yacho trabecular mapfupa. Panguva kutanga pavaipfuura chirwere chete sclerotized mapfupa tubular ari pfupa metaphyses uye sandara iri migove peripheral. Uyezve, padzakacherechedza dzisakarurama chisimbiso cranial pfupa, zvikurukuru nedambudziko paranasal mhango, kunyanya zvepuraimari uye frontal. Kukundwa chiri pachena uye shaya, zvinonzi aine kutyora nezvirwere uye zino kukura - vachinje nechivako yavo, insufficiently yakatanga midzi, vatsvaire migero uye in the zino. Kakawanda varwere kwachiremba varwadziwe ari makumbo uye kuneta kana kufamba. Marble mapfupa chirwere kuva nemigumisiro zvarinoita kukura vascular ezvinhu, sezvo kunyanya kukura zvemamiriro mapfupa rinenge zvishoma nezvishoma unotsiva hematopoietic tishu.

Best zvabuda chirwere pakurapa machena avapo mukuedza kuisirwa (kuisirwa) mwongo. Tinyatsobudirira kurapwa chirwere ichi usingatadzi parizvino dziripo. Kurapa chirwere ichi dzinowanzotsigi- zvainanga kwokungosimbisa tsandanyama uye huta hurongwa, uye vatakurwa kakawanda sezvo outpatients. Varwere vanoratidza physiotherapy, masaja uye kushambira. Nutrition kunofanira zvizere, akapfuma zvisaririra okunze uye mavhitamini, vanofanira kuva varipo vari Muterere, chizi, michero nemiriwo, muchero dzinongoitika uye muriwo facial. Vana vane chirwere ichi nenguva akatumira pachipatara pacho kurapwa.

Dzinokosha nzira yokudzivisa machena chirwere anorondedzera dzakabata perinatal chirwere gestation 8 mavhiki. Kudzivisa panowanikwa pfupa deformities uye pathological mitswe yaifanira guru bvunzo mu orthopedics.

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