Moebius chirwere: photo, zviratidzo, nechirwere, kurapwa

Zvakaoma kufungidzira munhu anogona nokuseka, kuchema uye kuratidza chero manzwiro. Zvisinei, pane vanhu vakadaro, uye vakaisa inotyisa chirwere - Moebius syndrome. Photos vanhu pakutanga kuaona ingaita zvachose kuipa, asi vararame kukurukurirana vanoziva kuti chiso chavo kuita chinhu zvachose.

Chinhu vachiberekwa anomaly kuti anova pamusoro chikuru chikonzero nokuda mamiriro emunhu ari cranial tsinga. Chiso rutivi rwomuviri - mumwe yakaipisisa uipi womunhu muviri. It kunoratidzwa kushaya chiso chedu, chiso rinoita kuti chando, uye sechinhu chokuzvivanza.

nhoroondo mashoko

Kokutanga mukurapa chirwere paakarondedzerwa 1892 kubudikidza wetsinga wokuGermany uye chiremba wepfungwa Paul Moebius. anomaly Izvi kushoma chaizvo, vaifanira kubva 10-20 paminiti mamiriyoni 1 kuzvarwa.

chiremba German Paul Julius Moebius akaberekwa muna 1853 muGermany uye vakagarako zvose hwake. Masayendisiti kudzidza kunotoda kukura zvishoma nezvishoma muviri, huta uye chirwere chepfungwa mu thyrotoxicosis. Description akaita oftalmoplegicheskoy migraine, achihudana chirwere Mobius.

Vakafunga Zvinokonzera

Wakakura zvikuru chimiro chirwere ichaongororwa kuva Moebius Syndrome, zvinokonzera iyo kusvikira kuguma mushonga kuchiri kuzivikanwa. Maererano nevaongorori uye nyanzvi ikatsemuka.

• Aimbova vanodavira kuti chikonzero ndiyo isiri kukura cranial tsinga.
• Ekupedzisira vanotenda kuti ichi tigume pamusoro pezvakaitwa zvinoparadza, dzichiri somugumisiro okisijeni nenzara mwana ari mudumbu.
• Third sezvo huru zvikonzero paumbwe chirwere anoratidza vanokara kusimudzira chiso motokari centre.

Moebius chirwere - chirwere akura chaizvo uye zvisinganzwisisiki chaizvo. Zviri vachiberekwa abnormality pakati tsandanyama dzechiso, nokuti chii chiri chose vasipo chiso chedu. The kuoma inogona single- kana kaviri madziro. Man hazvirevi sei zviwane, hapana kunyemwerera, hapana frowns, zvachose kuine manzwire.

In vana, taita yakatanga yakayamwa dzepanguva, havagoni kumedza dzavo zvokudya uye mvura nokuda simba mashandiro mutauro. Kazhinji hosha kunoitika mumhuri.

zviratidzo

Moebius chirwere - a vachiberekwa chetsinga rebipolar iri zvisinganyanyi kuitika. Vanhu vane zvokurwara ichi haakwanisi kufamba tsandanyama chiso, meso kumativi. chirwere ichi inotungamirira zvakakomba kutyorwa kuri zvetsandanyama nemapfupa ino uye deformation dzemumakumbo.

The chikuru zvekuchipatara zvinoratidza chirwere - a akavarambidza kufamba, asi kune vamwe, raidudzwa, vachisimbisa kuti uyu Moebius urwere zviratidzo:

• anatomical abnormalities;
• akaremara tsoka;
• dzikatadza pakuparadza uye yakayamwa;
• kutsinga dzinouya zvirwere zviri maonero;
• vachinetesa pamusoro mashandiro anoita mutauro;
• vasanyatsoona.

Uyewo, pane kutyora vestibular excitability nokushaya kukuvara secretion. Skin munhu anorwara pachiso Taut, finyamo-isina kunyange kana kuseka kana kuchema. Panyaya subcutaneous zvinyama hazvina kufamba, makona muromo nguva dzose kusiyiwa.

Kuremara ehomwe ari pamwe abnormality akadai syndactyly, clubfoot, brachydactyly uye yokuwedzera minwe. In rushoma kuoma kwacho kunosanganisira kunyanya tsandanyama rokumusoro chikamu chiso jira nokuti hapana droop sapamazuva vawana chirwere.

zvokurwara Diagnostics

Zvisinganyanyi kuitika anomaly akadai Moebius syndrome. Chirwere, saka, kunyanya kuvana vaduku, kwakaoma uye kazhinji kunotungamirira misdiagnosis, nengozi uye zvinoda kuvhiya kurapwa, akadai:

• palsy ;
• upofu;
• kusanzwa.

Ongororo uye zvimwe kurapwa vari kuitwa mirayiridzo iyi.

mushonga Modern achiri havagoni kuongorora zvizere chinokonzera chirwere ichi, saka, kurapa zvachose, zvakare, hazvibviri. Achiitisa kutsvakurudza uye kudzidza majini zvinhu zviri okutodza varwere padanho kunotsvaka muchitokisi kunotouraya.

Nhasi, vanachiremba Vakandikomberedza basa kubatsira vabereki nevana kutambura kubva chirwere ichi muna kwerunyararo kurarama panguva Pose pavaipfuura upenyu. Izvi zvinogoneka panguva kutaura kururamiswa, strabismus, gait.

Panguva Chaiyo chirwere kunokosha kwete chete nokuda kuziva miedzo dzakasiyana siyana zvarakasiya ari kukura, asi kuongorora kukura mupfungwa mashandiro uye kuziva mupfungwa zvigadziriswe uye zvekuchipatara zvirwere.

The chirwere pamusoro zvemamiriro kukura zvinosanganisira mupfungwa, dzidzo, kurapwa uye magene tsvakurudzo. Rave inoitwa kuona pachiyero sokunonoka kukura mupfungwa uye zvounhu, njere uye mutauro. Uyewo zvarinoita pokugadzwa kutaurirana pamwechete runotikurudzira chirwere vamwe pathological kuratidzwa, zera uye chetsinga ezvinhu omurwere.

Moebius Syndrome Treatment

Paradza ichi achinyengera chirwere kufanana Moebius urwere, kurapwa kunogona kubatsira chete zvomusejari. Hazvibviri kurapa zvachose chirwere, kuwedzera kune zvizorwa deformities, kusagadzikana pakuparadza nerevane nezvimwe zvinetso muviri kuti rinobatanidza chakaremara, varwere vanonzwa simba mupfungwa mupfungwa muupenyu. Kuderedza ichi anogona chete surgically.

Achibatsirwa epurasitiki Kuvhiya zvinokwanisika kuti uvhure hazvizivi chiso chedu, ipapo murwere achakwanisa kusimudza makona muromo, kunzwa pfungwa mufaro. Zvose chiso uye anoramba immobile uye kufara. Pane nyaya kuti pashure nzira dzakadaro, varwere vakanyadziswa nemigumisiro. Saka, asati oparesheni rinoitwa zvakazara azivisa murwere zvaizoitika uye pazvinobvira matambudziko.

Psychology evanhu ukama

oparesheni Izvi asi kunzwisisa kubva zvekushandisa chinoitwa, ayo nguva iri kashoma shoma pane maawa 8. Pashure yava rehabilitated varwere vari yevanorwara zvikuru kwemazuva maviri. Sezvineiwo, vanhu vakawanda vane mhosva iyi, kurarama sezvinongoita, basa, kutanga mhuri, vana.

Zvisinei, mashoko zvaanoita chiso chake yokukurukura uye munzanga kwadzakabva kunokosha chaizvo. Murwere hadzikwanisi kuva. Nokuda kuti munhu kunyimwa mukana kunyemwerera uye ane raidudzwa squint, izvozvo vakanzwisisa zvisiri sezvo azvakaita neshure munhu. Kunyange zvazvo pfungwa retardation chete 10% wevarwere.

Interlocutors zvakaoma chaizvo kunzwisisa kuti kuita mhando mashoko avo kukonzera uye anonzwa kuti panguva iyi munhu. izvi zvose kunokutadzisa kuipa pakukurukurirana, kuita varwere Moebius urwere kunze.

Moebius urwere muvana

Vana vaduku vanowanzopedzisira manzwiro akasiyana uye kazhinji, saka mwana pamwe Moebius urwere, iri pakarepo pachena. Haadi sei zviwane, kwete kuchema, haana kuseka, uye kunyange zvakaoma boira. Chete Ruzha anogona vaguely kunzwisisa chii zvinoda mwana.

Kubva pakuzvarwa, vana ava kutarisana vachiri, pane asymmetry yakajeka, muromo, maziso regai kuvhara, chenjerera zvinhu mwana anogona, unomutsa musoro wako chete. Kashoma kuchengetwa retardation pfungwa, murwere anofanirwa masaja hakusi chete kumeso asiwo mutauro, dzichiri nemakirasi nekunyatsotsanangura.

Zviratidzo ari rusvava

Moebius chirwere - nhaka zvokurwara wenhaka ndiyo autosomal recessive zvichidzika zvakazara. Kana urwere ichiri muchipatara mai vangu anoona kuti mimics yomwana tyisa, haana kuchema uye regai maziso ako nguva usiku. Vana ava vanowanikwa kanganisika zvakaipa:

• Kusavapo kana Fusion kuti minwe;
• deformation auricles;
• epicanthus.

Kunyange zvazvo chaizvo zvinokonzera hosha hakusati dzatangwa, vanachiremba vanoti rokutarisira zvinodhaka uye marwadzo zvinhu panguva pamuviri kunowedzera mukana chirwere. Zvizere Moebius chirwere mune vana havagoni murapwe asi nezera zvinova manyoro okuti.

Kurovedza kunatsiridza hwokukurukura

Nemhaka kurovedza chaiyo, iyo Rinorongawo Danish purofesa, mune vanhu vane Moebius urwere, kuvandudza kugarisana. Chinangwa kurovedza ndiko kuwedzera paralinguistic nzira yokukurukurirana kushandisa intonations siyana uye dzimwe nhengo dzomuviri.

Kubudirira kudzidzisa kwave vaudzewo kakawanda nokuongorora uye zvakawanika, panguva nhaurirano, varwere havachanzwi huta, regai Fuss uye huchawedzera vagadzikana. Maererano migumisiro varwere pachavo, vazhinji havanzwi kuvandudzika.

Co-munyori chirongwa kuna Ketlin Bogar, uyo akaonekwa Moebius syndrome. Kuvaka basa uye akava chiremba akabudirira pabasa rake, zviri chikuru chinangwa - kutanga chirongwa kuti chichabatsira kuchinja munzanga vanhu chirwere Moebius syndrome.