UtanoZvirwere uye Conditions

Systemic vasculitis: Zviratidzo uye kurapwa. Vasculitis - chii chirwere ichi?

Vasculitis - chii chirwere ichi uye kuti kunzwisisa sei muviri ichi?

vascular chirwere

midziyo nokuda siyana kunaka zvingakonzera kurasikirwa basa ravo, izvo kunokanganisa mamiriro yose muviri ropa.

Systemic vasculitis - nezvirwere izvo chokuita mwero vascular masvingo. Panguva ino Danho marudzi vanoverengeka chirwere ichi.

Marudzi systemic chirwere

Dzinozivikanwa mhando vascular Kumwe kuchinja kunotanga:

  1. The kukundwa nomumwe zvikamu zviri arteries svikiro kana chiduku-caliber inonzi periarthritis nodosa.
  2. Chirwere chinobata zvikurukuru pakati arteries uye nhumbi kufema turakiti uye nemapapu, itsvo uye chete ipapo ropa, richinzi Wegener kuti granulomatosis.
  3. Systemic vasculitis, vane zviratidzo zvinoratidza zvokurwara huru nhumbi muviri (kazhinji - the arteries musoro), inonzi hofori sero rwepanyama arteritis.
  4. Anogumbura pezvakaitwa huru arteries uye yeropa kunorondedzerwa se nechirwere Takayasu, kana aortoarteriit nonspecific.
  5. Maererano zvokurwara tsandanyama mhando arteries, ipapo chirwere so thromboangiitis obliterans.
  6. chirwere systemic iro pamwe zviratidzo zvakadai stomatitis, mumwe lesion munyama mumuromo uye yokubereka mucosa, uyewo kuchinja muziso wakanzi "chirwere Behcet kuti."
  7. Sema vasculitis.

Zvose pamusoro siyana dzinobatana nedzimwe zvinokonzera kuti chinokurwadzai kuchinja masvingo midziyo ropa uye kutyora mabasa avo.

Zvinokonzera chirwere

Kuziva mberi pfungwa kurapwa uye matanho, zvinokosha kuziva chii chinokonzera izvi kana kuti Kumwe kuchinja kunotanga rwengarava. Pakadaro, systemic vasculitis angava yakanaka mugumisiro murwere.

Kwete chaizvo kudzidza zvose zvinhu vanotsamwisa chirwere ichi, asi zvikonzero zvinoverengeka nei zvinganzi vaifungidzira:

  1. Systemic vasculitis sezvo muviri paakasangana pakushandisa zvimwe mishonga. Kumwe kuchinja kunotanga mudziyo masvingo kunogonawo kutsamwisa akabatwa chirwere kuti kare achishora kurapwa.
  2. Systemic vasculitis somunhu kuomesa vamwe vanotyaira zvinotapukira kuti dzabviswa.
  3. tsinga inogona kuparadzwa panguva zvirwere zvakadai reactive chearthritis, chinonzi systemic lupus erythematosus, anogumbura pezvakaitwa ari thyroid, chisingaperi autoimmune pathologies, Schwartz-Jampel urwere, uye pano neapo glomerulonephritis.

Zvose izvi kuona systemic vasculitis. Zviratidzo uye kurapwa zvirwere haina nguva dzose kwakabatana, nekuti vamwe zvinoratidza chirwere vari Isimba rakadini rinogona kubudiswa chimiro, apo vamwe, Ukuwo, dziri kuda kusaina isiri zviratidzo.

Chii chinoitika mumuviri? pathogenesis

The zvokurwara of vascular ezvinhu kunotoreva kuchinja anokuvadza mumuviri, ayo kuratidzwa panguva dzakasiyana zvokukura chirwere. Nyaya iripo ndeyokuti pangagara rinoburitsa kushoma nokuparadzwa dzairamba dzavo masvingo.

Mumwe mhando vasculitis akapa unobuda iine maitiro.

kuchinja chii pamwe ose?

  1. Kana urwere Behcet vakachengeta Zviratidzo zviri nemumuromo mhango, kunyanya stomatitis, izvo zvinobuda pamwe zvazvo. Chikamu chiratidzo chechipiri anganzi nemaronda ari scrotum zviri varume nevakadzi - ari nepanhengo uye vulva. Uyezve mucosa, kwakadai vasculitis pakawanda kunokanganisa eyeballs.
  2. Thromboangiitis obliterans achabatsirwa zvichemo dzevarwere, kukura lameness kana akangoerekana chiveve mumaoko.
  3. Aortoarteriit anopa nonspecific Migumisiro zvakadai kurwadziwa rezasi uye okumusoro kuviri, musana marwadzo, unopirwa mudumbu, uyewo kufenda uye zvinetso chokuita nemaziso.

Other siyana, zvichienderana zvakaoma, ndiwo anoita zvakafanana zviratidzo, asi anoda munhu mharidzo pakurapwa.

symptomatic mufananidzo

Symptomatology vascular chirwere unogona kushandura mufananidzo wako, zvichienderana chii localization kwacho uye pathologies pematanho navo.

Vasculitis chikonzero ganda rashes, uye pathological nenyonganiso munyika tsinga kunotoreva wakawedzera nehanya, izvo dzinosiyana hypersensitivity kuti yakaderera nehanya kana ayo kusavapo zvakakwana.

Kana ropa riparadzirwe uropi midziyo, parege Kurohwa uye mwoyo kurwiswa. Sema vasculitis kunoratidza sezvo kwese ane sema paakasangana tide.

Zviratidzo vascular zvokurwara

Kune vamwe zviratidzo zvinowanzovapo chero mhando vasculitis ndiko:

  • Mienzaniso kana zvakakwana kurasikirwa havi;
  • utera muviri iyo sokuti pasina chikonzero, uye pamwe kusakendenga;
  • nokukurumidza kuneta, zvose mumuviri tsika;
  • yakakwirira muviri tembiricha - yakaderera-sosaiti, dzimwe nguva anouya febrile chete;
  • ganda rakachenuruka, chokuita zvinopesana vakawanda kuparadzirwa pamuviri.

Chiizve kuti systemic vasculitis? Chii ichi chirwere uye sei kudzivisa izvozvo, unogona kuwanika zvimwe zvinhu. Somuenzaniso, mashoko nodular mhando vasculitis akaratidza tsandanyama vachirwadziwa zvose pamusoro muviri. Pain kunosvika kune mudumbu, kutsamwisa uremu, intestinal zvirwere, kurutsa, kuda kurutsa, uye, sezvo zvakaguma chirwere chepfungwa.

Wegner kwakaita granulomatosis, chinokurwadzai chirwere ari nasal mhango, kana kupfuura zvazviri, pachipfuva kwayo - pus, ropa uye madzihwa. maronda maitiro inogona kuitika panguva nasal mucosa. Ipapo chikosoro kunoitika, muchipfuva marwadzo, kupfupika mweya, itsvo kukundikana uye nevamwe.

ganda maronda

Kana pathological pezvakaitwa nemidziyo anokonzerwa ane sema maitiro, ipapo kwakadai vasculitis rinonzi ganda. Sei ganda vasculitis?

Dzaimiririrwa chirwere ane mhando dzakawanda kuyerera:

  • mhando rokutanga - nodosa necrotic kana Werther-Dyumlinga kunoratidzwa dermal site paganda ruvara pamwe rinokwanisa kucheneruka shava mumvuri;
  • wechipiri - sema arteriollit Ruiter, iyo inoratidza kwese eritrematoznymi rashes paganda, uyewo Hemorrhagic crusts, maronda, erosions pamwe tevera necrosis.

Chirwere pamusoro systemic vascular chirwere

The kusarudza chirwere nzira zvinofanira inobva kwokunze kuratidzwa vasculitis, asi kuona kwayo yakavanzwa siyana kushandisa mamwe matanho ari ongororo.

Kutanga anogona murwere vanofanira kuongororwa ropa kuti kuona kuchinja kwake. Kana quantitative zviratidzo zviri Chizenga zviri kudzika pane dzose, inoratidza kutanga neta neta pezvakaitwa pamuviri - kwakakomba kuomesa kwakaita vascular zvokurwara.

Kashoma, asi zvinoitika kana chirwere "systemic vasculitis" anoiswa pamusoro maererano kuongorora weti, kana kuzviona ropa masero matsvuku uye ropa masero machena.

Wechipiri munhu akaidza mutengo, asi kwete kunongokosha nechirwere, mumwe biopsy. Kuti izvi zvidaro, murwere nokuda nemaziso kuzviongorora atore chikamu mudziyo tishu.

Systemic vasculitis. Zviratidzo neMarapirwo

Zvichienderana kana sema vasculitis kana yechipiri kurapwa kuri ushandiswe nomumwe, uye akatungamirira kwete pakurapa chirwere zvakananga, asiwo kudzorerwa muviri wose, ayo payakarovera mu pakanyorwa vascular zvokurwara.

Chinangwa kurapa ndiko kuchaitwa kwakakwana zviratidzo nehosha, normalization midziyo ropa uye kufamba kweropa.

Zvinodhaka kuti zvinobatsira mune systemic vasculitis:

  • corticosteroid mishonga;
  • chemotherapeutic yomuchipatara;
  • immunosuppressants.

Kana zvimwe zvechisimba vasculitis zvakakodzera kuti kuitisa yevanorwara zvikuru uye kurapwa. Izvi zvinokosha kana kuti atadze kushanda zvakanaka dzinokosha nhengo dzakadai mwoyo, chitaka, mapapu, neitsvo. Muchiitiko chino, mumwe murwere nokumutswa achiteverwa symptomatic kurapwa.

ganda vasculitis vaifanira kubata imwe outpatient kana ari muchipatara, zvichienderana progressiveness ari pathological muitiro. Kubudirira chirwere ichi chichava matambudziko yakakura kururamiswa kune nzvimbo chirwere, kunoitika kare mune chirwere danho.

Murwere anofanira kutevedzerwa nemubhedha zororo uye nokutora zvinotevera mishonga:

  • antihistamines, kusanganisira mushonga zvakabatsirawo vasculitis vari "Promethazine", "Diphenhydramine", "Fenkarol";
  • karusiyamu gadziriro microelement - 10% karusiyamu chloride jekiseni kana gluconate mhinduro;
  • rutin, ascorbic acid.

Kana inefficiency kushandisa yakagozha kurapwa kushandisa gadziriro hormone akadai mishonga "prednisolone" uye "Dexamethasone".

Kana maperembudzi pamwe urikanwi uye necrotic urongwa, mishonga zvinosanganisira kukamura uchishandisa kushanda kunoita glucocorticoid mafuta (mafuta "Boron-naftalan" "methyluracyl" uye vamwe), epitelioplasticheskie gadziriro.

In-yakareba, asi basa kurapwa mune kosi ndiyo kushandiswa angiotroficheskih mari. mishonga iyi "dobesilate karusiyamu", "ksantinola nicotinate" uye vamwe.

Chii fungidziro chirwere ichi?

The fungidziro kunobva mhando vasculitis nekuomarara chirwere. Early chirwere uye nokukurumidza kunokwanisa yekudyidzana kurebesa upenyu murwere. Zvakakosha kuti chirwere uye kuva Zvakanyanya Kunaka Panguva Yepamuviri kurapwa zvaiitwa. Unofanira nemazvo kusarudza mishonga uye uwandu husingakuvadzi kuti vadzivise matambudziko uye marwadzo.

Hazvibviri kufanotaura zvaizoitika kwezvirwere zvakadai systemic vasculitis. Treatment vangangoshandira kuramba upenyu. Kazhinji, chirwere chacho chisingaperi, uye nguva exacerbation achiteverwa nguva kanganwiro. Disease vasculitis kazhinji haana kupera zvachose. Man nguva kumanikidzwa kushanyira chiremba uye kuzvidzora zviratidzo.

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