UtanoZvirwere uye Conditions

Gilbert kuti syndrome. chirwere chake, migumisiro

Gilbert kuti urwere, ndiko kuti chirwere? Gilbert kuti chirwere - zvikuru nyoro kunotoda musiyano wezvinyorwa dzichipfekeka hyperbilirubinemia. The chirwere rinoratidza UGT1A1 Gene mutation. Nokuti naye, enzayemu iri encoded pedyo UDP. Gilbert kuti chirwere kunoratidzwa zvinotevera:

  1. Yakakwirira kwevari ropa bilurbina
  2. Kukwana kukundikana glyukuroniltransferazy
  3. Kusavapo hepatic kuchinja
  4. Kuderera kwemitambo yakakwirira bilirubin nokuda kuitwa phenobarbital

Nokuti nguva yokutanga Gilbert kuti chirwere chakawanikwa muna 1901, vanachiremba French Gilbert Nicolas Augustin uye Lereboullet P. Vakaziva chirwere se "imwe cholehemia mhuri". Pashure paizvozvo, akanga pfungwa mazita mashoma, asi akamira pamusoro Gilbert kuti syndrome. chirwere ichi rinowanzoberekera nevanhu makore 25-30 makore.

Zviratidzo zvemo zvirwere

Muvanhu, pane kuneta, zvakarurama yokumusoro quadrant colic kuitika. The chikuru nekuratidza chirwere ndiye kufunganya uye vakarondedzera ruvara. Dzimwe nguva zvinoitika kuti yellowness haasi kuoneka, uye munhu anodzidza pamusoro chirwere chete pashure pacho akabata nokukanganisika muviri. Kune mhando mbiri chirwere: episodic uye refu. Kana munhu panyama overloading muviri wako, jaundice kunogona kuitika. Uyezve, doro, nzara angava "kutanga" nokuda kukura chirwere.

Gilbert kuti urwere kuongorora chirwere.

Kunopindirana bilubirin munguva chirwere chingava pachiyero 21-51 mmol / L, sezvamakaropafadzwa zvinokwanisika kuwedzera huwandu 85-130 micromoles / fő. Kuziva chirwere ichi, unofanira kupfuura rinokosha kuongorora chirwere. Rinogona pakubhadhara anoverengeka.

  1. Test pamwe nenzara. Ainyanya kushandiswa pasi-mafuta zvokudya, zvichida - achitsanya kwemaawa 48. Saka wevasungwa kuti bilirubin muropa inowedzerawo.
  2. Test pamwe pentobarbital. Kushandiswa mishonga iyi inotungamirira kweiyi ari enzayemu basa glyukuroniltrasferazu, nokudaro achidzikisa padanho bilirubin.

pakurapa chirwere

Chero vavashandire, zvarwo, kwete, nokuti zvakakurumbira ane muviri, kwete chirwere. Just sick contraindicated imwe mutoro, tinofanira kutevera rinokosha kudya. Doro munhu akadaro anofanira hakubvumidzwi nekuti kwavo kushandiswa kungaita kuti kukura chirwere. Asi zvinokosha kuyeuka kuti vari panyaya Gilbert kuti chirwere haumanikidzwi kuramba majekiseni. Panguva amplification jaundice vanachiremba varayire imwe kudya, vhitamini ARV ushandiswe.

Gilbert kuti urwere Migumisiro

Vaya vakawana chirwere Gilbert raMwari, migumisiro mubereko, uyewo sei chirwere huchachinja chiropa. Zvimwe zvinokonzerwa haagoni kuva zvachose, asi zviri nani kuita Ultrasound chiropa, uyewo muedzo kuti bilirubin ropa. Kuti chiropa rakaramba pamusoro kuonekwa kuti Gilbert kuti urwere, unofanira kuomerera kudya, uye woga woga kuti maekisesaizi. Dzimwe migumisiro chirwere anogona kuratidza sezvo kupfuura ruvara steatosis. Zvikurukuru, migumisiro aya kuchengetwa nevanhu. Saka, varume kutambura chirwere vanofanira akuteerere utano hwavo.

Ndezvipi Zvaifungidzirwa akaisa varwere?

chirwere ichi chinogona kuonekwa musiyano pakati vasingambooni chakaipa nazvo. Vanhu ava vanonzi vave vashoma utano, kunyanya mune vavashandire havafaniri. Pasinei chokwadi kuti hyperbilirubinemia hunogona kuchengetedzwa kuti upenyu, Gilbert kuti chirwere haiiti kuti rufu. Pane mukana psychosomatic zvirwere, uye cholelithiasis. Migumisiro chirwere ichi sevasingazivi kusvikira makore 20, asi nguva dzose achiperekedzwa munhu, zvikuru kuti anogona kuita nhodzera chikonzero. Chinonyanya kukosha ndechokuti chirwere ichi haina kunyanya tinzwe pane basa nevanhu.

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