Hirschsprung nehosha: Zviratidzo kuvana, photo, zvinokonzera, nechirwere, kurapwa

Mumwe undistributed pathologies ndiyo chirwere Hirschsprung raMwari. Zviratidzo zviri vana anotaurwa kugara kupatira. Dzimwe nguva chirwere chinogona kuitika nedzevakuru. Asi kupfuura zvose vana vanotambura nawo. Chinhu vachiberekwa chirwere iri nhaka. Zvinonzi chirwere zvikurukuru vakomana. It akaratidza pakarepo pashure pokuberekwa. Kana marapirwo ndiyo chete inoshanda kuvhiya kupindira.

zvokurwara mamirire

Hosha chinorondedzerwa muna 1887 neboka Danish wevana Harold Hirschsprung, ane zita kwapera chirwere ichi uye zita. Pakutanga, mamiriro ezvinhu anonzi vachiberekwa gigantism muura. Zvokurwara ane rimwe zita. Inonzi vachiberekwa agangliozom muura. Chii chirwere Hirschsprung muna vana?

Zviratidzo (Mufananidzo kunoratidza zvokurwara) vari zvinosiyana munhu unhu, izvo madziro muura havasi kuumbwa tsinga ganglia. Kureva ivo kudzora tsandanyama vari kusundwa kuti ironge zvokudya ura. Kusavapo ganglion tsinga kunokonzera tsandanyama rinenge kuti havasi kushanda. Somugumisiro, zvokudya hachivaiti kuburikidza huru ura. zvokurwara iyi inonzi chirwere Hirschsprung kuti. Zviratidzo zviri vana varehwa sezvo kupatira, noutachiona uye kuzvimba.

Kuitika Hirschsprung nehosha - 1 muna 5000. Ndiyo chete mumwe zviuru zvishanu vachangoberekwa vanotambura nechirwere ichi. Most kazhinji chirwere, sezvaratidzwa pamusoro apa, zviri akaonekwa mune vakomana.

zvokurwara Zvinokonzera

Kunyange zvazvo chirwere paakarondedzerwa muna 1887, zvakatora makore akawanda kuti kuziva zvinokonzera kuti chidzoke uye kukura chirwere ichi.

Doctors kupa siyana kuti kutsamwisa kukura kwakadaro zvisingafadzi zvirwere sezvo Hirschsprung nehosha mune vana.

Zvinokonzera chirwere:

1. Somugumisiro kuferefeta zvakatanga kuti zvokurwara inotungamirwa kunoitika kunyange utero. Tsinga namasumbu, izvo achazadzisa zvakafanira mashandiro ari kugaya, vari yakaumbwa muna mudumbu kubva 5 kusvika 12 vhiki pamuviri. Mune zvisingawanzoitiki Muzviitiko, kukura masero etsinga munyika zvomudumbu ezvinhu ane mwana haasi wakakwana. Huru ura, havasi kuumbwa. The zvinokonzera chirwere ichi haisi kujekeswa. Zvinofungidzirwa kuti nokudaro akaratidza kunotouraya mu DNA.
2. Cherechedzawo hunhodzera iri panowanikwa chirwere ichi. Kana pane zviitiko hosha mumhuri, ipapo mukana wokuti mwana achaberekwa kurwara, zvakakwirira zvikuru. Kunyanya kana ari mudumbu ari munhurume, nekuti vakomana vanorwiswa chirwere ichi 4-5 nguva kakawanda kupfuura vasikana.
3. In kunzvimbo rwuchiwanzwa nemwaranzi, vana vakawanda vaine Hirschsprung chirwere.
4. Factor kukanganisa pakuonekwa chirwere ndiye Down kuti syndrome.
5. Zvokurwara anogona kuva somugumisiro kwemakemikari anobudiswa zvirwere zviri amai.

kupatsanura zvirwere

Pane zvakawanda siyana zvokurwara ichi sezvo Hirschsprung nehosha (muvana). Zviratidzo kuti anowanika mune mwana, zvingaratidza kuti chirwere ane mhando.

Pane zvinotevera siyana Hirschsprung chirwere:

1. Ndanyarara hangu - kupatirwa kuitika vaduku. Kurarama navo achishandisa kwokucheneswa enemas kwenguva refu.
2. Subkompensirovanaya - enema hauna kufambisa kushanda. Somugumisiro, kudzikisirana kunoitika uremu rutapudzo. Murwere anonzwa kuchema uye kurwadziwa mudumbu. In chimiro ichi maperembudzi vaichengeta nechitarisiko dyspnea, kupererwa neropa. Muviri kaviri kuchinja.
3. Asthma - the ura havagoni kucheneswa nokucheneswa enemas uye laxatives. Pashure nezviyero izvi, kunzwa Kutambudzika dzakaderera mudumbu uye bloating Havamboregi. Kana iwe change kudya kana rinorema kurovedza angatanga inopinza intestinal mhingaidzo. In-Murwere vana chimiro ichi chirwere wakaiswa pa subtotal uye zvachose kukundwa.
4. Chenjera - bowel mhingaidzo mu vacheche.

chirwere zviratidzo

The chirwere kungazviratidza mumazuva okutanga muupenyu. Somuenzaniso, kana muura haana ndokudururira ari achangoberekwa mumazuva okutanga muupenyu, zvinokosha kuongorora mwana kuziva zvinokonzera uye zviratidzo. Zvichida ichi ndicho chirwere Hirschsprung raMwari.

Zviratidzo kuvana, uyo vanofanira kuteerera, seizvi. Mwana anoramba chikafu. Ari kuva kupatira. Ura havana kudururwa. Zvimba dumbu. Pane wheezing. Ichi chiratidzo chokuti mwana Hirschsprung chirwere. Zviratidzo kuvana kuitika, kazhinji mukati rokutanga mwedzi upenyu.

Zvisinei, chirwere anogona kuita pacharo ainzwa zvikuru gare gare. Naizvozvo, unofanira kunyatsotevera kuongorora mamiriro utano mapfupa. Pakarepo kutaura vanachiremba dzako kana ukaona zviratidzo chakatodzana chirwere Hirschsprung mune vana.

Zviratidzo zvirwere kuti munogona vacheche pasi gore rimwe:

• kupatira;
• pokumbononotswa kuwana uremu;
• muchiridza kwezvakanga mudumbu;
• kurutsa;
• manyoka.

Mukana panowanikwa chirwere kunoratidzwa gare gare muupenyu.

Achiperekedzwa zvakawanda zvive anotevera zviratidzo:

• chisingaperi kupatira;
• chitsiko kubuda RIBBONS;
• kuti ura kumbobvira zvakazara kubudiswa.

Chiizve kuteerera?

The chikuru chiratidzo chirwere huru ura zviri chisingaperi kupatira. Kana zvokudya breastmilk chiratidzo kurege kuitika. Inorwadza zviratidzo muka chete panguva apo nopindirana zvokudya chakaunzwa zvokudya mafufu. It hwamunoita kushanda ane enema. Asi kubatsira ari kuchengetwa chete tanga. Zvadaro shandisa mukana enema hunoguma kupa achida mugumisiro.

Kushandura ukuru uye chimiro mudumbu, riri pasi dzinoshungurudza dumbu - zviri zvakare zviratidzi kuti munokosha achiteerera. Kana dzakayerera iri misha muura uye dumbu anotora asymmetric mugari chimiro.

Kurutsa kuti kunoitika nezvirwere ichi, zvinobatsira muviri yavangabata chetsoka, nomuchetura iye.

chirwere Hirschsprung anogona kuonekwa uyewo vakura. Varwere ava vanowanzoda kutambura kubva pauduku kupatira. Vanoda mushonga kubatsira bowel kufamba. Vanonyunyuta tichinzwa kurwadziwa mudumbu, kazhinji atarisana flatulence.

zvokurwara Diagnostics

Zvakakosha kuti nokukurumidza kuziva chirwere.

Chirwere kuti Hirschsprung nehosha mune vana zvinosanganisira nzira dzakadaro:

1. Rectal ongororo. Zvinoratidza iri mugaranhoko chinhu chinu. Pane kuwedzera basa pamusoro sphincter.
2. Sigmoidoscopy. Kuonekwa nezvipingamupinyi ari vanachandagwinyira zvikamu mugaranhoko, kana kusavapo shoma mutsvina yadzo.
3. X-ray. Anoona bundu ndokuwedzera loop ari muura.
4. Ergography. muura zvishwe yakawedzera kusvika 10-15 masendimita ari dhayamita. Zvinoshandisa zano rose abdominal mhango.
5. Kufamba barium kuturika. The Musiyano mumiriri inopfuura nomunyika nemudumbu, arambe ari muura. Kubva ipapo chinhu refu anobva nguva. Dzimwe nguva kunonoka kusvika 5 mazuva.
6. Ultrassom intestinal nzvimbo.
7. Anorectal manometry. Akayera kumanikidzwa vari ura.
8. Kolonosokopiya. Yakasimbiswa kana akaramba achishandisa mashoko airatidza X-ray.
9. A biopsy of rectal rusvingo Swanson. Kutsunga kuvapo etsinga ganglia ari muura ndeyokuwana kukamuka muura rusvingo.
10. Histochemistry. Anogadza basa enzayemu acetylcholinesterase tishu.

kuchinja mabatiro

Regai kuvimba kurapa kwakadaro. kurapwa Hirschsprung nehosha mune vana rinoitwa kakawanda chete kuvhiyiwa. Kuchinja kurapa Kazhinji ndipiyona ndimugadzirire mamwe kuvhiyiwa.

Preparatory kurapwa kunosanganisira:

1. A wakananga kudya, kudya. Varumbidzwa kudya muriwo, michero, nomukaka zvinogadzirwa, zvokudya haakonzeri gasi inotungamirwa.
2. Massage, physiotherapy, jimunasitikisi. Ivo ude intestinal motility.
3. Yokuzvinatsa enema.
4. Intravenous kwokubatsira proteinaceous medicaments uye electrolyte mhinduro.
5. Mavhitaminzi.

kuvhiya kurapwa

Kureva, hunobvumira murwere mushure vapore kubvisa Hirschsprung chirwere.

The kupfuura dzakakodzera makore mwana kunorapwa ichaongororwa kwemakore 2-3. Gadzirai murwere kunorapwa kumba. Vhiki shomanana, unofanira kutevera zvokudya, bowel kufamba vachibatsirwa enemas. Special kudya hazvo ndakarumbidzwa ari kupinda chiremba kuti inorangarira makore mwana uye zvose zvaidiwa muviri, uyewo padariro pakukura ichi chisingafadzi chirwere sezvo Hirschsprung nehosha mune vana.

Ndavhiyiwa, mwana anofanira kuonekwa nachiremba mukati 2 years. Panguva ino, chiremba anoita munhu kudya mwana wako. Vabereki vanofanira kuramba ziso mwana chair. Zvinokurudzirwa kuisa mafufu enema ose zuva, pane imwe chete nguva. Zvakakodzera kukudziridza dzepanguva bowel sangano.

mhedziso

chirwere Hirschsprung ndiyo ngozi. Zvinokwanisa kuratidzwa pakarepo. Panyaya iyi mwana kutambura kubva abdominal kurwadziwa, kuda kurutsa, kurutsa, yakareba. Vabereki vanofanira kuongorora Nguva rwecheya uye mwana kuchangotanga kutyorwa kuenda kwachiremba.