Shavishavi chirwere: epidermolysis bullosa

Epidermolysis bullosa (Eb), kana sezvazvakanyorwa kunzi, shavishavi chirwere - ichi haiwanzowaniki chaizvo nhaka nyonganyonga. Vana ava vanonzi vana kungozvifunga. Kana zita iri une dzimwe shamwari dzinonakidza, chirwere choga hakusi nemachira zvinofadza. Kutaura zvazviri, varwere epidermolysis bullosa vanopedza upenyu hwavo hwose vari chinorwadza chirango. The chikonzero - ganda ravo, kusimba sezvo shavishavi mapapiro.

Zvinosuruvarisa chirwere ndiye "shavishavi chirwere" haigoni disinfected. Nokuti zvikuru midzi muna majini chechetere. Vana vakadaro vanoda chaiyo kutarisirwa: zvachose nyoro ezvinhu, zvipfeko neshangu. MuRussia, chirwere ichi chisingarapiki haana kunyange kuiswawo pakati pemazita kupfuura isingawanzowanikwi zvirwere. Zvisinei, pane mari chaiyo kubatsira vana Butterfly "Bella."

Gore negore yakawanda mari iri kumamwe uhu, kuti zvimwe kubatsira vana vane chirwere "shavishavi chirwere". Mifananidzo varwere vanogona kuonekwa munyaya ino, uye mabhuku zvesayenzi zvokurapa. Zvisinei, mashoko ari epidermolysis bullosa haana kugamuchira kuparadzirwa wakakodzera Russia uye Kishi nyika.

Chirwere "shavishavi chirwere" Hazvizivikanwi kuti voruzhinji. Vashoma anogona kunyange kureva zita rayo kwakatooma - epidermolysis bullosa. Zvisinei, vana ava vane zvose pamusoro Russia uye Kishi nyika. Mumwe nomumwe varwere pamwe chete dambudziko: vanachiremba veko havazivi kuti vanoita, chirwere chinonzi "inenge", uye kwete nguva dzose vakatendeka kune mhando chirwere. Uye dzimwe nguva amai vake kunyange kuvanza vana ava, inotungamirira kurufu rwavo nokuda kutarisirwa kukodzera.

shavishavi chirwere kunoratidzwa pakuonekwa dzevanhu ganda mapundu sefuro. Zvichienderana matema ndivo mhando anotevera pamusoro Epidermolysis Bullosa (Eb):

1. Simple. Zvinonzi akaumba napachivivo chokumusoro nzvimbo ganda. The ganda richikora pamusoro emichindwe uye inotsikwa netsoka. Matema anogona aumbwa kunyange pamuromo.
2. Border. Kunenge pamusoro dermal-epidermal Junction. In zvakakomba chirwere matema anogona kuonekwa pamasvingo yegurokuro, ura uye genitourinary turakiti.
3. Dystrophic. Matema kuoneka pamabvi, maoko, emaoko, mucous membranes, kunogona yegurokuro, kukonzera zvinetso kukura uye kudya kunovaka. Izvi mhando zvakare dzinoratidzwa Fusion minwe nezvigunwe.

Syndrome shavishavi - mugumisiro inotungamirwa emunhu puroteni paganda, kana rayo kusavapo. Uyewo chinokonzera chirwere chingava kwakanga kwatangwa Gene mutation.

Pakuzvarwa, ganda mwana anorwara kunzvenga sezvo paganda nyoka. Chokwadi, ichi chinokonzera kuvhunduka maitiro ari mai. Vazhinji kungoti vanoramba vana vanorwara iri maternity wadhi achiri. Asi mukana kupona mwana pamwe chirwere epidermolysis bullosa mumba vana zvachose razero. Vazhinji vevana vakafa panguva isiri kutarisirwa. Pashure pezvose, vana ava vanofanira kunyatsoongorora chaizvo kubata.

Chinonetsa nguva pavarwere - ndiro zera kusvika 3 years. Zvishoma nezvishoma, pamwe nekodzero hanya, ganda coarsens. A vana vaduku kana kuedza kukambaira vose rakanaka mabvi uye maoko. Skin Maronda akasiyana uye rinokwatuka kure, zvichiita kurwadziwa. Vana vakadaro vanogona kunyange kukwazisana sezvo aingovawo munhu. With achikura, zvishoma nezvishoma kudzidza kuzvidzivirira. Pazera 3 makore oupenyu kunova nyore.

Zvisinei, varwere chakakomba muchimiro Epidermolysis Bullosa kutarisana daily kurwadziwa uye kuvaviwa, chisingafaniri kubatsira kunyange antihistamines. Uyezve, mumwe matatu mazuva, vanofanira kutsungirira zvakafanira uye anorwadza dressings. Vana ava, kufanana nevamwe vose nechirwere chisingarapiki, dzinokosha. Vane meso hazvidaviriki, zvimwe kubva marwadzo ichi sokusingatsungiririki, hatigoni kunzwisisa.