Zviratidzo chokuita hemolytic-uremic chirwere chacho kurapwa

Saka, chii chaunofanira kuziva kutanga nokuda hemolytic-uremic syndrome (rakapfupikiswa - Hus). Doctors vanoti chirwere ichi kunonyanya nezviratidzo zvitatu: chenjera renal kukundikana, hemolytic kupererwa neropa, thrombocytopenia. Zvinofanira kucherechedzwa kuti ekupedzisira chikabviswa inowanzopiwa hwakaratidzwa pachena zvikuru. Maperembudzi panoonekwa kunyanya vana vaduku.

zvinogoneka zvikonzero

Huru zvinhu dzinoitwa hemolytic-uremic chirwere - imwe sema kwomusikirwo mishonga, uyewo chaikonzerwa noutachiona. Hazvina musoro kuti hosha anotanga kuva pashure rikwanise kufema uye mudumbu zvirwere kana Varwere pakugamuchira inorwisa mabhakitiriya. Maererano pathogenesis pamusoro Hus, pachinhu ichi, mukuru kukosha wanamatira pamberi autoimmune siyana. Mune zvimwe zviitiko, vangave kunyange kukonzera systemic microangiopathy.

symptomatology

Ndezvipi zviratidzo kazhinji kunokonzerwa hemolytic uremic chirwere? Zvinofanira kucherechedzwa kuti weboka chirwere navanachiremba conventionally muzvikamu zvitatu nguva. Chokutanga, prodromal, anogona kugara kubvira zuva rimwe kwevhiki mbiri. Chechipiri, vanonzi "dambudziko nguva" - kubva munhu nhatu. Ipapo kupora nguva (kana rufu) murwere auya.

Chikamu chirwere rose kutanga afanane chepfu uye achabatsirwa zviratidzo zvakadai kurutsa, zvikuru dumbu marwadzo, manyoka pamwe zvisaririra ropa. Vamwe varwere vari Danho ichi chakaratidza kugwinha, hope uye kunyange kurasikirwa chavanoziva. Pashure prodromal nguva pavarwere zhinji kunouya zvinooneka kupora. With haemolytic uraemic chirwere chokuita vanachiremba sezvo haemolytic kupererwa, thrombocytopenia, uye renal maronda. Vanachiremba vanoti kunotoda mufananidzo, sezvo mutemo, kusiyaniswa imwe polymorphism. Mune vamwe varwere, zvingaratidza nesimba hemolytic dambudziko, vamwe - zviratidzo chakasimba renal kukundikana. Common nyaya dzose vaiona chiratidzo hemolytic kupererwa neropa - ikaramba pakati Hus.

Hemolytic-uremic chirwere muvana rechipiri chikuva dzinoratidzwa yomumvuri pallor ganda. In pamberi jaundice dzinogona kuonekwa hyperbilirubinemia. Kazhinji Direct Coombs 'bvunzo akaipa, vaburusira Chizenga, nhamba erythrocytes ipfupi. Uyewo, varwere kazhinji mhino iri kubuda ropa.

Diagnostics

Doctors kazhinji rokuongorora Hus, yakavakirwa chikuru nzira nhatu: kuvapo hemolytic kupererwa, thrombocytopenia purpura uye uremia. Kazhinji, kuti kurapwa mufananidzo wakafanana nowenyika Moshkovitsa syndrome (chirwere cheitsvo, ropa clots midziyo, uye zvichingodaro. D.), With musiyano chete ari kuti ekupedzisira Kazhinji vana vakura, uye mikrotrombozov rinowanikwa kunonyanya mumwoyo uye chiropa.

Hemolytic uremic chirwere: kurapwa

Kudzvinyirira autoaggression - ndicho chikuru chinangwa kurapwa. Kazhinji, vanachiremba vakatuma zvose mauto kuti kudzivirira intravascular coagulation. Zvakanaka kubatsira heparin uye prednisolone. Kana mishonga asingadi kubatsira, izvozvo kunoratidzwa hemodialysis.