Chii - a chirwere Rokitansky-Otto Küstner? Syndrome Rokitansky-Otto Küstner: zvinokonzera, zviratidzo, kurapwa

Surrogacy anobvumira vana nevakadzi nezvikonzero zvoutano havagoni pamuviri pachavo. nhamba yavo, maererano nenhamba, yakawedzera kubva gore negore. Mumwe zvikonzero zvinokufadza basa rimwe anoberekera mumwe mukadzi mwana ndiye Rokitansky-Otto Küstner syndrome. The zvinokonzera chirwere, zviratidzo zvacho uye dzinokosha nzira kurapwa ichakurukurwa munyaya ino. Uchadzidzawo kana mukadzi chirwere ichi vana.

zvokurwara mamirire

Syndrome Rokitansky-Otto Küstner-Meyer-Hauser - isingawanzowanikwi gynecological chirwere. rine mazita masayendisiti uyo akapa rondedzero yakatodzama pamusoro zvokurwara muzita rayo. Uyewo mabhuku ezvokurapa pane anoreva zvakafanana chirwere: kusangana nekutsi kwemukadzi Surgery, aplasia pamusoro dumbu. Zvisinei, havasi kuratidza kutyorwa zvose mumuviri, zvakafanana nezvaiitwa vamwe syndrome. Uyezve, kusangana nekutsi kwemukadzi Surgery anogona kuitika nokuda kuzvimba kana kuvhiya. Kazhinji, zita chirwere zvizere kuderedza maviri mazita masayendisiti kana okuti "MRKH chirwere" wokutanga.

The zvokurwara kunoratidzwa kwakakwana kana rushoma pasina dumbu, uyewo 2/3 of nyinyo. Muchiitiko chino, pane kukura izere ovaries uye sikarudzi. Also inochengetwa yechipiri pabonde maitiro (muviri bvudzi riri hadzi mhando, chipfuva). Rokitansky-Otto Küstner chirwere kunokwanisa kuonekwa kashoma (nyaya imwe zviuru 5. Girls vachangozvarwa).

nhoroondo mashoko

The Kurondedzera rokutanga musi chirwere shure 1829 gore. chiremba German Carl Mayer yakati kuti kusangana nekutsi kwemukadzi aplasia kunowanzoguma dzakasiyana-siyana zvokukura abnormalities. Papera chinguva, muna 1838, rimwe pathologist kubva Austria Karl of Rokitansky chirwere tsananguro vakawedzera. Akazvipira kuti kana chirwere ichi Uyewo vasipo dumbu, ovaries asi vane kukwanisa kushanda zvakazara. Muna 1910, chiremba German German Kyustner waitsanangura iripo mashoko ari pamusoro chirwere, achiwedzera wake pazviri. The gayinakorojisiti zvinorondedzerwa mienzaniso kakawanda akabatana aplasia uterine malformations itsvo kukura. Muna 1961, Purofesa Zhorzh Hauzer kubva Switzerland akataura kuti shoko rokuti "Otto Küstner Rokitansky-Mayer-urwere". Scientist akabudisa ake zvaanorumbidza wevarwere vakawanda vane chirwere ichi, izvo akataura kusava kune varume mahormone pavarwere. Muna 1977, Houser pakutanga akapa rondedzero atypical musiyano pakati zvokurwara. Kupiwa mupiro guru masayendisiti, kuti chirwere akanzi kuti vawana mazita mana.

Zvinokonzera chirwere

Kunyange embryonic munguva fetus vakaisa anatomical zvikanganiso kuti zvaizobatsira Otto Küstner-Rokitansky syndrome. Photos of vana vane chirwere ichi pashure pokuberekwa regai nedziya zvavo utano vezera. Maererano Muller pfungwa, fetus pabonde nhengo kuva panguva mwedzi wechipiri pashure pamuviri. Matambudziko akaipa zvikonzero zviri pamusoro muviri mumwe pamuviri panguva ino zvinogona kukonzera zvirwere zvakasiyana-siyana mune vana. On panowanikwa munhu chirwere uyewo chinobata connective zvinyama dysplasia mudumbu umo nenyonganyonga waro mamiriro kunoitika. Kumwe kuchinja kunotanga kutungamirira kukudziri- chakaremara nhengo, mumwe kuratidzwa unova Otto Küstner-Rokitansky syndrome.

Zvii zvinobatsira panowanikwa chirwere ari mwana panguva yepamuviri?

1. toxicosis Strong.
2. HIV iri mai.
3. Zvakaipira pamuviri.
4. Kutora mamwe mishonga (yakadai corticosteroids).
5. Doro.

The chirwere haisi semhosva nhaka zvirwere. Zvisinei, mune kurapwa tsika pane zviitiko apo zvokurwara akaonekwa vakadzi vanoverengeka dzemhuri imwe.

Clinical zvinoratidza chirwere

Otto Küstner-Rokitansky chirwere ari kutanga kuratidza pakuyaruka apo yokuyaruka muviri. Vasikana zvishoma vakagumisa mazamu, kuchinja nhamba, pane muviri bvudzi revanoshamwaridzana munzvimbo. Akazivisa yechipiri zvepabonde maitiro Usabvumira vanofungidzirwa zvinetso zvoutano. Vasikana vakawanda nenguva dzirikure kurwadziwa munzvimbo dzakaderera mudumbu nzvimbo, Kutambudzika rezasi musana. Zvisinei, kuti kusavapo kumwedzi kunotungamirira kutsvaka rubatsiro kubva gayinakorojisiti. Chimwe chikonzero kushanyira nyanzvi kungava dambudziko rakapfava hunhu. Kundikana kuedza zvepabonde kakawanda kuguma kunotevera kuti perineum kana atsamwira kuti dundira. Kuratidza underdevelopment mitumbi inogona wokugaya dumbu pamwe yakaoma fallopian sepombi. Inenge 40% of akanaka pabonde MRKH chirwere pamwe malformations nezvezvimwe zvinetso zvedundira.

kupatsanura zvirwere

Kufanana nevamwe anomalies ose embryo kukura vazhinji, Rokitansky-Otto Küstner chirwere ane madhigirii siyana kuti zvakaoma. Kusimba neimwe iri pakutsvaga kwokuomerwa fetus abnormalities. Kune zvitatu siyana chirwere:

1. Typical MRKH syndrome (64% vose nyaya). It kunoratidzwa aplasia pamusoro dumbu uye nyinyo.
2. Atypical MRKH syndrome (24% vose nyaya). In chirwere ichi, vasikana asimo dumbu uye nyinyo, pane dysfunction pakati ovaries.
3. MURCS-kuwadzana (12% vose nyaya). Ndicho wakakura zvikuru chimiro urwere, izvo kunoratidzwa zvinetso pamusoro apa uye nechimwe vanokara Kugadzirwa marangwanda.

Chimiro chirwere kunotema racho kuchirapa nzira uye kunobatsira vanachiremba kuti kufanotaurwa kwechimwe kupora.

nzira nechirwere

Chii rokuongorora zvinokosha kuzosimbisa chirwere Rokitansky-Otto Küstner? Zviratidzo chirwere havasi chete yokuona nayo chirwere. murwere kuongororwa chinotanga kutarisana vaongo-. Muna 75% kacho haitauri chero kutyorwa, nokuti yechipiri zvinhu anoenderana dzemunharaunda. Zvadaro, kuongorora gynecological chair. Vasikana vane hymen zvokuongorora rinoitwa pachishandiswa vachifunga. Nokuti kwese pfupi nyinyo syndrome (kusvika 2 cm), izvo hakusi kuguma cervix gwara. Chimwe chirwere nzira iri rectal kuongororwa, panguva iyo chiremba Yatanga Kuongorora fallopian chubhu uye uterine mhango. Nzira Izvi zvinoita kuti vaongorore mwero inotungamirwa zvomukati.

Kugara nokuyerwa basal tembiricha kunobatsira kuona Pasika kumwedzi kuzosimbisa zvizere mashandiro ari ovaries. Mukuwedzera, chiremba prescribes nemiedzo nokuda hormone, MRI uye pelvic Ultrasound ropa. In kunyanya zvakakura Muzviitiko kungada laparoscopic kuongorora chirwere.

Nzira kurapwa

Pane nzira imwe chete kurapa Rokitansky-Otto Küstner chirwere - yepedyo epurasitiki. Operation pamusoro paumbwe nyinyo rinonzi colpopoiesis kwaari kutarisira vanachiremba vane akarwawo kuti XIX remakore. Pakutanga, kuvhiyiwa anoshandiswa kurapa vakadzi vane vakachengetedzwa dumbu mabasa. In varwere izvi ropa haana kubva pamuviri, uye zvishoma nezvishoma vaunganidza munyika abdominal mhango. Somugumisiro, havana kunge nechirwere neoplastic urongwa, dzakanga achiperekedzwa kurwadziwa uye matambudziko akasiyana-siyana.

Pari vakabata colpopoiesis nenzira mbiri:

1. Kuwedzera pamusoro nyinyo achibatsirwa ane Inflatable chibharuma. The oparesheni anotora nguva refu. Implementation Its zvinokwanisika chete kana kuti kusangana nekutsi kwemukadzi kureba haasi asingasviki 4 cm.
2. Inotungamirwa neovaginy chikamu sigmoid muura kana ganda mudumbu. Modern ruzivo kubvumira kuti aruramise zvikanganiso pasina abdominal cheka - laparoscopically. Vanachiremba kakawanda vanosarudza nzira iyi, paumbwe rakagadzirwa nevanhu nyinyo.

The yakanaka zera nokuda colpopoiesis ndiyo nguva kubva 16 kusvika 21 makore. nguva ino, chokupedzisira kuibvisa iri muviri. Chinangwa the kusangana nekutsi kwemukadzi epurasitiki - vakwanise vakadzi kunakidzwa zvizere pabonde upenyu. Kuti adzivise imperforate yayo haafaniri kusiya nguva pabonde, nguva nenguva kupfuura bougienage muitiro.

Matambudziko pashure pokuvhiyiwa

Ndezvipi matambudziko pashure pokuvhiyiwa anogona kusangana varwere chirwere kuti "Rokitansky-Otto Küstner urwere"? Pakurapa chirwere dzimwe nguva pamwe chero migumisiro yakaipa. Colpopoiesis - iri kuvhiyiwa. Sezvinongoita mimwe muchimiro kuvhiyiwa, zvinokwanisika kukura yematambudziko. Pakati pavo, ivo Zvinonyanyozivikanwa sepsis uye peritonitis. Uyewo, varwere vakawanda pashure nzira yokurapa, vanachiremba akaonekwa Fusion neovagina masvingo. zvokurwara Izvi anovandudza nokuda kwokushayiwa dzose upenyu pabonde. Naizvozvo, vanachiremba vanoti zvakasimba kuti vakadzi kusaregeredza pabonde.

Kushurudzira pashure kupora

Zvakachinja mumuviri kuti kuitika vakadzi vane chirwere che "Rokitansky-Otto Küstner chirwere" haabvumiri kuita dzokubereka basa takasununguka. Zvisinei, nzira ano IVF uye surrogacy rubatsiro varwere vakadaro vane vana chaivo. Masayendisiti vachangobva akazivisa migumisiro yakanaka munhu anenge apa dumbu nokuisazve kushandiswa. Papera kanguva, zvichida, transplantation muviri kuchabatsira vakadzi achinyengera chirwere ichi pachavo kubereka vana.

Kushaya mbereko uye chirwere Rokitansky-Mayer-Otto Küstner

Ndinogona kuita vana vane chirwere ichi? mubvunzo uyu unomuka kubva pavakadzi vazhinji vari vakatarisana zvokurwara. Nokufamba kwenguva, mumwe nomumwe wavo anoda kuedza pamusoro basa mai. Vakadzi vazhinji vane chirwere ichi hazvigoni kubereka mwana. Kana ovaries vari kushanda zvakanaka, saka nyanzvi dzinoti varwere vane mukana wokuzvidzivirira kuti mabasa ane anoberekera mumwe mukadzi mwana. Panyaya iyi mwana chakaumbwa?

In padariro wokutanga purogiramu anoberekera mumwe mukadzi mwana uye mukadzi achirwara ari ushandiswe mishonga hormone. Kushandisa zvinodhaka mukati imwe nguva kunoita kuti synchronize kumwedzi zvinogara dzavo. Ipapo mukadzi zai chirwere MRKH artificially inseminated pamwe dzisingaoneki wake. Mumazuva mashomanana hwavo "rakura" mune svikiro kuti mimics Zvivako zviri fallopian sepombi. Pashure pemazuva matatu, nyanzvi dziri kutanga gadziriro kwerubwinyo rwakagara rwuripo-muchibereko: kuona bonde embryo, kuvapo chromosomal urema uye nhaka zvirwere. Nezuva reshanu yakatanga embryo Kutamiswa kupinda dumbu amai kuberekerwa mwana nomumwe. Mune zvimwe zviitiko, miviri podsazhivanie Somuenzaniso, pazuva rechitatu uye reshanu.

Nhamba tuvana Kutamiswa dzingasiyana zvichienderana nokunaka majini zvokunyama, zera murwere. Akumbirwa yomukadzi, tsva zai vanosangana cryopreservation pakuvhiya. Somugumisiro pamuviri ichi munyika muna 9 months pane mwana ane utano. Zvisinei, nzira iyi ine zvose vatsigiri uye vaimupikisa.

Yoga vanofanira kufunga surrogacy. In zhinji kushandiswa makiriniki pane anonzi vakadzi chawo, vanoda kupa zvakafanana basa. Kazhinji ndiwo vasikana vaduku, utano. Chimwe zvikonzero kushandisa imwe kiriniki yakadaro chirwere Rokitansky-Otto Küstner-Meyer-Hauser. Photos ramangwana kuberekerwa mwana nomumwe vanaamai vanogona kuwanikwa Database ichi. Yose muitiro, kubva kusarudzwa zvingakanganisa biomamy uye kupedza pamuviri, kudzora centre nevatungamiri. Saka zvakanaka kutaura nyanzvi, pane kuita kutsvaka kuzvidzora. Chete nenzira iyi inogona kuramba chivimbo utano yemberi mwana wako.

To muchidimbu

Syndrome Rokitansky-Mayer-Otto Küstner - chinhu majini chirwere inozivikanwa kusavapo kana hypoplasia pamusoro dumbu uye nyinyo. Vasikana vazhinji vasati pakuyaruka havatombozivi nezvezvinetso zvoutano. Amenorrhea unovaparira kuona chiremba. Yakanga iri panosvikira panguva nyanzvi Ivo vokutanga vazive kuvapo urwere akadaro. Kudivi rimwe, zviri kwese kuti maldevelopment pamusoro dumbu uye nyinyo, uye kuno rumwe - kuvapo yechipiri bonde unhu. Nhasi, pane dzakawanda marapirwo zvirwere. Vose vari kuramba vari nani uye vaisanganisa. The kurapa chirwere ndiko kubvisa kuremara kubudikidza revanoshamwaridzana mapurasitiki. Somugumisiro, murwere anogona kubvisa mupfungwa uye vasiri matambudziko, noupenyu uye kunyange vana. Panyaya zvapedzisira pfungwa, zvinoda rubatsiro munhu anoberekera mumwe mukadzi mwana.