Proteus Syndrome: Zviratidzo neMarapirwo Nzira

To musi, Proteus chirwere anoonekwa isingawanzowanikwi chaizvo nemagene chirwere, icho pamwe ane tyisa kukura mabhonzo, tsandanyama uye connective munyama. Zvinosuruvarisa chirwere uye kurapwa zvirwere zvakadai - wakaoma chaizvo uye kwete nguva dzose zvinoita muitiro.

mushonga Modern, zvinozivikanwa chete kuti Proteus chirwere ane nhaka chirwere uye kusonganirana mutation majini. Zvisinei, nomazviri panowanikwa kuchinja izvi haisi aizvinzwisisa.

Proteus Syndrome: A nhoroondo shoma

Kokutanga chirwere wakadaro anorondedzerwa muna 1979. Ndipo apo Maykl Koen yakawanikwa vanenge 200 zviitiko ichi chirwere pasi pose. Yakanga mudzidzi uyu uye akapa zita chirwere. Proteus - mwari gungwa mungano yechiGiriki. Uye, maererano ngano dzekare, huMwari ichi aigona kuchinja chimiro uye kukura muviri wake pachake.

Proteus Syndrome: Zviratidzo

Kutaura zvazviri, chirwere angaperekedzwa dzakasiyana-siyana kuchinja uye nenyonganiso. Kazhinji, vana vanorwara vanoberekwa zvakakwana kuipa, uye chete nemakore chinja kutanga. Sezvineiwo, pane chimwe nechimwe, kuti zvingaratidza kuva akasiyana. Mune vamwe varwere, chirwere chokugara nhaka anoratidzwa netsaona, sezvo pasina zvimwewo zviratidzo usipo. varwere vamwe, nekusiyana, anenge zvose ake upenyu chirwere kusanzwa.

Sezvambotaurwa, Proteus syndrome (hunomirirwa) pamwe nezvokukura zvinyama - zvinogona tsandanyama, mapfupa, ganda, node nemidziyo ropa, mafuta tishu. Growths anogona kuonekwa zvinenge kwese. Somuenzaniso, pane kazhinji kuwedzera kukura musoro uye maoko nemakumbo, shanduko wavo wenguva chimiro.

Zvinofanira kucherechedzwa kuti hunotarisira vanhu upenyu ipfupi. Ndivo tichikurumidza matambudziko kweropa maitiro (embolism, yakadzika tsinga thrombosis), uyewo kenza uye goiter.

By pacharo, Proteus chirwere haakonzeri kunonoka kukura. Asi somugumisiro ndichibvunza overgrowth pakati zvinyama angava yechipiri maronda ose tsinga.

Proteus Syndrome yaro kurapwa

Nokuti kutanga zvinokosha kuziva kuti mangwanani chirwere kunokosha chaizvo. Kwokutanga maperembudzi inoziviswa, nani mukana mwana ane upenyu hwakanaka. Kufanana zvose nhaka uye vachiberekwa zvirwere, dambudziko harisi chete mhinduro - hazvibviri kubvisa pasi syndrome. Asi nzira mushonga ano kuchabatsira kurwisa pfungwa zviratidzo.

Somuenzaniso, kana kukura remafupa rinenge scoliosis, zvakasiyana kureba Mbabvu zvichida akapfeka chaiwo vachibatsira mano kubatsira kukurira dambudziko. Kana maperembudzi chokuita abnormalities ari kweropa ino kana bundu, murwere vanofanira kuramba pasi kuramba pokudzora chiremba.

Kazhinji kushandiswa uye zvomusejari kurapa. Somuenzaniso, kushandisa oparesheni anogona kugadzirisa nokuruma, wakaatapudza mapfupa minwe, kuti munhu anogona kushandisa maoko maviri. Dzimwe nguva unofanira kugadzirisa pfupa uye connective zvinyama zviri pakati thorax, kuti tipedze murwere kubva kuzvinetso zvokufema uye pakuparadza.

Chero zvazvingava, chirwere ichi zvinoda uchizvichenjerera uye kutarisirwa. The chete nzira kurebesa upenyu uye kuvandudza unhu kwayo.