UtanoZvirwere uye Conditions

The chirwere cystic fibrosis. Chii?

Cystic fibrosis zvichida ndicho chirwere rakajairika munyika, iri nhaka. Wakatanga akarondedzerwa American wevana Dorothy Anderson muna 1938. The yepamutemo zita - fibrosis of rwatata.

Cystic fibrosis: chii?

The kwaita nyanzvi chirwere chokuita mutation ane puroteni kuti anoita chloride chiteshi nerevane ari kuitika mumvura uye electrolyte nepakati kufema masero, nemudumbu, rwatata, Urinary maitiro uye chiropa. Kana kusingarapiki kuchinja mapuroteni tiite yakawanda nechitarisiko secretion mumasero zvikuru yaiitwa yakapfupikiswa, zvinova zvakaoma ayo voga, pane mhirizhonga munyika zvomukati. Cystic fibrosis hakuchinji kazhinji bronchopulmonary hurongwa.

Masvingo tsinga dzinokudziridzwa kwazvo kuzvimba siyana giravhiti collapses ari unobatanidza puranga, uye bronchiectasis vari akaumba nokukurumidza. At chenguva plugging zvikuru viscous sputum bronchiectasis vari kuva kakawanda, pakupedzisira kuwedzera hypoxia uye pulmonary neBP.

Cystic fibrosis: chii uye chii vari zviratidzo?

Zvinokosha kucherechedza kuti zviratidzo hosha irege kuva pakarepo pachena. Doctors vanowanzotanga kurapa vanhuwo bronchitis, asi pakupedzisira zvinoitika kuti ichi hachisi here, uye cystic fibrosis. Help iri ipapo zvakasiyana zvachose unhu. Kutambura kubva chirwere dzinoratidzwa:

  • chinokosha lag mu kwomuviri;
  • chisingaperi zvirwere zviri kufema nadzo (kusanganisira sinusitis uye bronchitis);
  • polyps mumhino;
  • pfungwa nomuviri zvemwana asati;
  • kufema kukundikana.

Cystic fibrosis: chii uye sei chirwere?

Chokwadi, pakururamisa yakarurama zvokuongorora pasina kuongorora kwakakodzera nyore kuita. On the dambudziko nani nenzira Integrated nenzira. Assays izvo ushandiswe nokuda kuziva miedzo cystic fibrosis:

  • ziya bvunzo;
  • chloride wevasungwa;
  • chymotrypsin mu pachituru;
  • mafuta acids zviri pachituru;
  • DNA Diagnostics.

Cystic fibrosis: chii uye sei kubatwa?

Panguva iyoyo, zvachose kukunda chirwere ichi hazvibviri. Asi kana imi hanya varwere vane cystic fibrosis inopiwa pamusoro nguva, kunyange chirwere ichi munhu anogona kurarama upenyu nokururamisira refu.

Varwere All kubatwa unhu kudya uye kurovedza muviri. Diet uye mutoro seti nyanzvi nomumwe. Zvadaro Mabatirwo cystic fibrosis mberi, yakavakirwa zviratidzo. Chinangwa chikuru chemusha vanachiremba pano - kudzivirira blockage pamusoro mapapu uye kudzivirira mhingaidzo pamusoro nemudumbu. varwere vose panguva imwe chete vari vakanyorwa ari dispensary.

Basic mushonga zvinodhaka: enzymatic, Anti fungal uye antibacterial nevamiririri. Sezvo kurapwa panyama kazhinji ushandiswe vibration masaja mhiri chipfuva uye inokosha jimunasitikisi.

Pane mukana?

Maererano nedzimwe mishumo avhareji youpenyu hunotarisira murwere kuRussia - makore 15-18. Mune US Somuenzaniso, pamwe chirwere chakadai murwere anogara avhareji yemakore 28-42.

Asi mushonga, sezvo tichiziva, asingadi mira. Masayendisiti munyika yose chirwere ichi nokungwarira ari kudzidzwa. Zvinonzi vakatenda vazhinji varwere izvi, vakaberekerwa 2000, mushonga ano chinogona pave makore 45-55 kare hunogutsa.

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